Publications

• Real-world insights from a cohort of approximately 2000 individuals who were analysed using a freely available next-generation sequencing anaemia screening programme.
  Br J Haematol
  03/09/2025 Authors: Balciuniene J; Yilmaz S; Chonat S; Grace RF; Soff GA; Ravindranath Y; Glader B; Bianchi P; McGee B; Agarwal AM
• Persistent splenic-derived IgMs preferentially recognize factor VIII A2 and C2 domain epitopes but do not alter antibody production.
  J Thromb Haemost Volume: 23 Page(s): 440 - 457
  02/01/2025 Authors: York ES; Dratch BD; Ito J; Horwitz SM; Emamian S; Ambarian JA; Gill S; Jones J; Chonat S; Lollar P
• CD47 regulates antigen modulation and red blood cell clearance following an incompatible transfusion.
  Front Immunol Volume: 16 Page(s): 1548548
  01/01/2025 Authors: Jajosky RP; Covington ML; Liu J; Chai L; Zerra PE; Chonat S; Stowell SR; Arthur CM
• Fatal thrombotic microangiopathy during induction for acute myeloid leukemia: A case report and review of vascular complications in germline GATA2 haploinsufficiency.
  Br J Haematol Volume: 206 Page(s): 368 - 371
  01/01/2025 Authors: Frost EL; Chonat S; Williams KM; Aumann W; Stevenson J; Yin J; Schniederjan M; Arnold S; Schoettler ML
• Harnessing the potential of red blood cells in immunotherapy.
  Hum Immunol Volume: 85 Page(s): 111084
  11/01/2024 Authors: Jajosky RP; Zerra PE; Chonat S; Stowell SR; Arthur CM
• Comparative clinical efficacy and safety of biosimilar ABP 959 and eculizumab reference product in patients with paroxysmal nocturnal hemoglobinuria.
  Am J Hematol Volume: 99 Page(s): 2108 - 2117
  11/01/2024 Authors: Kulasekararaj A; Lanza F; Arvanitakis A; Langemeijer S; Chonat S; Tombak A; Hanes V; Cao J; Miller MJ; Colbert A
• Real-World Application of Recently Proposed ASTCT/CIBMTR/EBMT/APBMT Consensus Risk Stratification for Transplantation-Associated Thrombotic Microangiopathy in Children.
  Transplant Cell Ther Volume: 30 Page(s): 929.e1 - 929.e6
  09/01/2024 Authors: Schoettler ML; Ofori J; Bryson E; Spencer K; Qayed M; Stenger E; Bidgoli A; Chonat S; Westbrook A; Williams KM
• Age, GVHD prophylaxis, and timing matter in thrombotic microangiopathy after haematopoietic cell transplantation-Asecondary CIBMTR analysis.
  Br J Haematol Volume: 205 Page(s): 243 - 255
  07/01/2024 Authors: Schoettler ML; Westbrook A; Watkins B; Stenger E; Qayed M; Chonat S; Williams KM
• COping with acute sickle cell hemolysis.
  Blood Volume: 143 Page(s): 2452 - 2453
  06/13/2024 Authors: Chonat S; Stowell SR
• Pharmacokinetics, pharmacodynamics, efficacy, and safety of ravulizumab in pediatric paroxysmal nocturnal hemoglobinuria.
  Blood Adv Volume: 8 Page(s): 2813 - 2824
  06/11/2024 Authors: Chonat S; Kulagin A; Maschan A; Bartels M; Buechner J; Punzalan R; Richards M; Ogawa M; Hicks E; Yu J
• Pediatric transplant-associated thrombotic microangiopathy health care utilization and implications of eculizumab therapy.
  Blood Adv Volume: 8 Page(s): 1220 - 1233
  03/12/2024 Authors: Schoettler ML; Lehmann L; Kao P-C; Chen N; Jodele S; Chonat S; Williams KM; London WB; Duncan C; Dandoy C
• Diagnosis and management of pyruvate kinase deficiency: international expert guidelines.
  Lancet Haematol Volume: 11 Page(s): e228 - e239
  03/01/2024 Authors: Al-Samkari H; Shehata N; Lang-Robertson K; Bianchi P; Glenthj A; Sheth S; Neufeld EJ; Rees DC; Chonat S; Kuo KHM
• D-dimer and sinusoidal obstructive syndrome-novel poor prognostic features of thrombotic microangiopathy in children after hematopoietic cellular therapy in a single institution prospective cohort study.
  Am J Hematol Volume: 99 Page(s): 370 - 379
  03/01/2024 Authors: Schoettler ML; French K; Harris A; Bryson E; Deeb L; Hudson Z; Obordo J; Chandrakasan S; Parikh S; Watkins B
• Compassionate Use Narsoplimab for Severe Refractory Transplantation-Associated Thrombotic Microangiopathy in Children.
  Transplant Cell Ther Volume: 30 Page(s): 336.e1 - 336.e8
  03/01/2024 Authors: Schoettler ML; Patel S; Bryson E; Deeb L; Watkins B; Qayed M; Chandrakasan S; Fitch T; Silvis K; Jones J
• Voxelotor improves red blood cell functionality in children with sickle cell anaemia: An ancillary study of the HOPE-KIDS 1 trial.
  EJHaem Volume: 5 Page(s): 125 - 130
  02/01/2024 Authors: Chonat S; Fields E; Baratz H; Watt A; Pochron M; Dixon S; Tonda M; Brown C; Archer D
• Frequency of HLA-DR+CD38hi T cells identifies and quantifies T-cell activation in hemophagocytic lymphohistiocytosis, hyperinflammation, and immune regulatory disorders.
  J Allergy Clin Immunol Volume: 153 Page(s): 309 - 319
  01/01/2024 Authors: Nguyen TH; Kumar D; Prince C; Martini D; Grunwell JR; Lawrence T; Whitely T; Chappelle K; Chonat S; Prahalad S
• Antibody-mediated antigen loss switches augmented immunity to antibody-mediated immunosuppression.
  Blood Volume: 142 Page(s): 1082 - 1098
  09/21/2023 Authors: Jajosky RP; Patel KR; Allen JWL; Zerra PE; Chonat S; Ayona D; Maier CL; Morais D; Wu S-C; Luckey CJ
• DARATUMUMAB FOR THE TREATMENT OF REFRACTORY AUTOIMMUNE HEMOLYTIC ANEMIA IN PEDIATRIC PATIENTS POST-HEMATOPOIETIC CELL TRANSPLANT
  Volume: 70 Page(s): S214 - S215
  06/01/2023 Authors: Yoo J; Obordo J; Schoettler M; Qayed M; Hughes K; Harris A; Spencer K; Parikh S; Chandrakasan S; Chonat S
• USE OF CAPLACIZUMAB IN PEDIATRIC THROMBOTIC THROMBOCYTOPENIC PURPURA PATIENTS
  Volume: 70 Page(s): S139 - S139
  06/01/2023 Authors: Graciaa S; Sidonio R; Zerra P; Rollins M; Briones M; Chonat S
• CLINICAL OUTCOMES OF CHILDREN AND ADOLESCENTS WITH PAROXYSMAL NOCTURNAL HEMOGLOBINURIA
  Volume: 70 Page(s): S134 - S135
  06/01/2023 Authors: Saleem N; Graciaa S; McElfresh P; Arnold S; Schoettler M; Briones M; Chonat S
• Sickle cell disease is a risk factor for transplant-associated thrombotic microangiopathy in children.
  Blood Adv Volume: 7 Page(s): 1784 - 1795
  05/09/2023 Authors: Schoettler M; Stenger E; Spencer K; Lutterman D; Rumbika S; Jones J; Haight A; Parikh S; Qayed M; Watkins B
• Factor H autoantibodies contribute to complement dysregulation in multisystem inflammatory syndrome in children (MIS-C).
  Am J Hematol Volume: 98 Page(s): E98 - E101
  05/01/2023 Authors: Zerra PE; Stowell J; Verkerke H; McCoy J; Jones J; Graciaa S; Lu A; Hussaini L; Anderson EJ; Rostad CA
• Efficacy and safety of biosimilar ABP 959 compared with reference eculizumab in adults with PNH
  Volume: 201 Page(s): 4 - 5
  04/01/2023 Authors: Kulasekararaj A; Lanza F; Arvanitakis A; Langemeijer S; Chonat S; Pan J; Chow V; Saportas Y; Henary H
• Storage differentially impacts alloimmunization to distinct red cell antigens following transfusion in mice.
  Transfusion Volume: 63 Page(s): 457 - 462
  03/01/2023 Authors: Maier CL; Jajosky RP; Patel SR; Verkerke HP; Fuller MD; Allen JW; Zerra PE; Fasano RM; Chonat S; Josephson CD
• Pulmonary Manifestations and Vascular Changes in Pediatric Transplantation-Associated Thrombotic Microangiopathy.
  Transplant Cell Ther Volume: 29 Page(s): 45.e1 - 45.e8
  01/01/2023 Authors: Schoettler ML; Saldana BD; Berkenkamp L; Chonat S; Watkins B; Rotz SJ; Simons D; Graf E; Rossi C; Cheng J
• Characteristics and outcomes of pediatric oncology patients at risk for guardians declining transfusion of blood components.
  Cancer Rep (Hoboken) Volume: 6 Page(s): e1665
  01/01/2023 Authors: Stevenson J; DeGroote NP; Keller F; Brock KE; Bergsagel DJ; Miller TP; Cornwell P; Fasano R; Chonat S; Castellino SM
• Clinical features and neurological outcomes in pediatric immune-mediated thrombotic thrombocytopenic purpura: A report from a large pediatric hematology center.
  Pediatr Blood Cancer Volume: 69 Page(s): e29992
  12/01/2022 Authors: Graciaa S; Adeagbo S; Fong G; Rollins M; McElfresh P; Zerra PE; Bennett C; Josephson CD; Briones M; Fasano RM
• Compassionate use narsoplimab to treat transplant associated thrombotic microangiopathy in a pediatric patient with multi-organ failure
  Volume: 57 Page(s): 350 - 350
  11/01/2022 Authors: Schoettler M; Bryson E; Deeb L; Qayed M; Watkins B; Chandrakasan S; Chonat S; Williams K
• Mitapivat in adult patients with pyruvate kinase deficiency receiving regular transfusions (ACTIVATE-T): a multicentre, open-label, single-arm, phase 3 trial.
  Lancet Haematol Volume: 9 Page(s): e724 - e732
  10/01/2022 Authors: Glenthj A; van Beers EJ; Al-Samkari H; Viprakasit V; Kuo KHM; Galactros F; Chonat S; Porter J; Zagadailov E; Xu R
• Sustained effect on hemoglobin levels and reduced transfusion burden maintained in patients with pyruvate kinase deficiency on mitapivat in a long-term extension study
  Volume: 45 Page(s): 138 - 139
  09/01/2022 Authors: Grace RF; Glenthoj A; Barcellini W; Verhovsek M; Rothman JA; Morado AM; Layton DM; Andres O; Galacteros F; van Beers EJ
• A virtuosic CADENZA played by sutimlimab.
  Blood Volume: 140 Page(s): 933 - 935
  09/01/2022 Authors: Chonat S; Stowell SR
• Evaluating ravulizumab for the treatment of children and adolescents with paroxysmal nocturnal hemoglobinuria.
  Expert Rev Hematol Volume: 15 Page(s): 385 - 392
  05/01/2022 Authors: Yoo JJ; Chonat S
• Clodronate inhibits alloimmunization against distinct red blood cell alloantigens in mice.
  Transfusion Volume: 62 Page(s): 948 - 953
  05/01/2022 Authors: Arthur CM; Patel SR; Sharma A; Zerra PE; Chonat S; Jajosky RP; Fasano RM; Patel R; Bennett A; Zhou X
• Mitapivat versus Placebo for Pyruvate Kinase Deficiency.
  N Engl J Med Volume: 386 Page(s): 1432 - 1442
  04/14/2022 Authors: Al-Samkari H; Galactros F; Glenthj A; Rothman JA; Andres O; Grace RF; Morado-Arias M; Layton DM; Onodera K; Verhovsek M
• Health-related quality of life and fatigue in children and adults with pyruvate kinase deficiency.
  Blood Adv Volume: 6 Page(s): 1844 - 1853
  03/22/2022 Authors: Al-Samkari H; van Beers EJ; Morton DH; Eber SW; Chonat S; Kuo KHM; Kollmar N; Wang H; Breakey VR; Sheth S
• Risk of Disseminated Gonococcal Infections With Terminal Complement Blockade.
  J Pediatr Hematol Oncol Volume: 44 Page(s): e493 - e495
  03/01/2022 Authors: Graciaa SH; Graciaa DS; Yildirim I; Chonat S
• T-follicular helper cell expansion and chronic T-cell activation are characteristic immune anomalies in Evans syndrome.
  Blood Volume: 139 Page(s): 369 - 383
  01/20/2022 Authors: Kumar D; Prince C; Bennett CM; Briones M; Lucas L; Russell A; Patel K; Chonat S; Graciaa S; Edington H
• Molecular and phenotypic diversity of CBL-mutated juvenile myelomonocytic leukemia.
  Haematologica Volume: 107 Page(s): 178 - 186
  01/01/2022 Authors: Hecht A; Meyer JA; Behnert A; Wong E; Chehab F; Olshen A; Hechmer A; Aftandilian C; Bhat R; Choi SW
• Heme interferes with the regulatory properties of complement factor I in human plasma
  Volume: 141 Page(s): 180 - 181
  01/01/2022 Authors: Gerogianni A; Poillerat V; Dimitrov J; Chonat S; Sandholm K; Ekholt K; Ekdahl KN; Mollnes TETE; Mohlin C; Roumenina L
• Heme Interferes With Complement Factor I-Dependent Regulation by Enhancing Alternative Pathway Activation.
  Front Immunol Volume: 13 Page(s): 901876
  01/01/2022 Authors: Gerogianni A; Dimitrov JD; Zarantonello A; Poillerat V; Chonat S; Sandholm K; McAdam KE; Ekdahl KN; Mollnes TE; Mohlin C
• Emerging therapeutic and preventive approaches to transplant-associated thrombotic microangiopathy.
  Curr Opin Hematol Volume: 28 Page(s): 408 - 416
  11/01/2021 Authors: Schoettler M; Chonat S; Williams K; Lehmann L
• Correction to: T CellEpsteinBarr Virus-Associated Hemophagocytic Lymphohistiocytosis (HLH) Occurs in NonAsians and Is Associated with a T Cell Activation State that Is Comparable to Primary HLH.
  J Clin Immunol Volume: 41 Page(s): 1979
  11/01/2021 Authors: Shamriz O; Kumar D; Shim J; Briones M; Quarmyne M-O; Chonat S; Lucas L; Edington H; White MH; Mahajan A
• T Cell-Epstein-Barr Virus-Associated Hemophagocytic Lymphohistiocytosis (HLH) Occurs in Non-Asians and Is Associated with a T Cell Activation State that Is Comparable to Primary HLH.
  J Clin Immunol Volume: 41 Page(s): 1582 - 1596
  10/01/2021 Authors: Shamriz O; Kumar D; Shim J; Briones M; Quarmyne M-O; Chonat S; Lucas L; Edington H; White MH; Mahajan A
• ACTIVATE-T: A PHASE 3, OPEN-LABEL, MULTICENTER STUDY OF MITAPIVAT IN ADULTS WITH PYRUVATE KINASE DEFICIENCY WHO ARE REGULARLY TRANSFUSED
  Volume: 106 Page(s): 30 - 30
  10/01/2021 Authors: Glenthoj A; Van Beers EJ; Al-Samkari H; Viprakasit V; Kuo KHM; Galacteros F; Chonat S; Porter J; Gheuens S; Beynon V
• Pyruvate kinase deficiency in children.
  Pediatr Blood Cancer Volume: 68 Page(s): e29148
  09/01/2021 Authors: Chonat S; Eber SW; Holzhauer S; Kollmar N; Morton DH; Glader B; Neufeld EJ; Yaish HM; Rothman JA; Sharma M
• Marginal zone B cells mediate a CD4 T-cell-dependent extrafollicular antibody response following RBC transfusion in mice.
  Blood Volume: 138 Page(s): 706 - 721
  08/26/2021 Authors: Zerra PE; Patel SR; Jajosky RP; Arthur CM; McCoy JW; Allen JWL; Chonat S; Fasano RM; Roback JD; Josephson CD
• Are We Forgetting About IgA? A Re-examination of Coronavirus Disease 2019 Convalescent Plasma.
  Transfusion Volume: 61 Page(s): 1740 - 1748
  06/01/2021 Authors: Verkerke H; Saeedi BJ; Boyer D; Allen JW; Owens J; Shin S; Horwath M; Patel K; Paul A; Wu S-C
• COMPLEMENT IN THROMBOTIC MICROANGIOPATHIES
  Volume: 68 Page(s): S111 - S111
  06/01/2021 Authors: Graciaa S; Zerra P; Fasano R; Chonat S
• CHARACTERISTICS AND OUTCOMES OF PEDIATRIC ONCOLOGY PATIENTS AT RISK FOR TRANSFUSION REFUSAL
  Volume: 68 Page(s): S97 - S98
  06/01/2021 Authors: Stevenson J; DeGroote N; Choudhury T; Keller F; Brock K; Bergsagel DJ; Miller T; Cornwell P; Chonat S; Castellino S
• Comorbidities and complications in adults with pyruvate kinase deficiency.
  Eur J Haematol Volume: 106 Page(s): 484 - 492
  04/01/2021 Authors: Boscoe AN; Yan Y; Hedgeman E; van Beers EJ; Al-Samkari H; Barcellini W; Eber SW; Glader B; Yaish HM; Chonat S
• Congenital dyserythropoietic anemia type I: First report from the Congenital Dyserythropoietic Anemia Registry of North America (CDAR).
  Blood Cells Mol Dis Volume: 87 Page(s): 102534
  03/01/2021 Authors: Niss O; Lorsbach RB; Berger M; Chonat S; McLemore M; Buchbinder D; McCavit T; Shaffer LG; Simpson J; Schwartz JH
• An automated approach to determine antibody endpoint titers for COVID-19 by an enzyme-linked immunosorbent assay.
  Immunohematology Volume: 37 Page(s): 33 - 43
  03/01/2021 Authors: Ho AD; Verkerke H; Allen JW; Saeedi BJ; Boyer D; Owens J; Shin S; Horwath M; Patel K; Paul A
• The pyruvate kinase (PK) to hexokinase enzyme activity ratio anderythrocyte PK protein level in the diagnosis and phenotype of PK deficiency.
  Br J Haematol Volume: 192 Page(s): 1092 - 1096
  03/01/2021 Authors: Al-Samkari H; Addonizio K; Glader B; Morton DH; Chonat S; Thompson AA; Kuo KHM; Ravindranath Y; Wang H; Rothman JA
• Antigen density dictates RBC clearance, but not antigen modulation, following incompatible RBC transfusion in mice.
  Blood Adv Volume: 5 Page(s): 527 - 538
  01/26/2021 Authors: Arthur CM; Allen JWL; Verkerke H; Yoo J; Jajosky RP; Girard-Pierce K; Chonat S; Zerra P; Maier C; Rha J
• Thrombocytosis with acquired von Willebrand disease in an adolescent with sickle cell disease.
  Clin Case Rep Volume: 9 Page(s): 457 - 460
  01/01/2021 Authors: Yee MEM; Batsuli G; Chonat S; Park S
• Eculizumab for complement mediated thrombotic microangiopathy in sickle cell disease.
  Haematologica Volume: 105 Page(s): 2887 - 2891
  12/01/2020 Authors: Chonat S; Graciaa S; Shin HS; Newton JG; Quarmyne M-O; Boudreaux J; Tang A; Zerra PE; Rollins MR; Josephson CD
• Role of complement in alloimmunization and hyperhemolysis.
  Curr Opin Hematol Volume: 27 Page(s): 406 - 414
  11/01/2020 Authors: Chonat S; Mener A; Verkerke H; Stowell SR
• Characterization of the severe phenotype of pyruvate kinase deficiency.
  Am J Hematol Volume: 95 Page(s): E281 - E285
  10/01/2020 Authors: Al-Samkari H; van Beers EJ; Morton DH; Barcellini W; Eber SW; Glader B; Yaish HM; Chonat S; Kuo KHM; Kollmar N
• Eculizumab for complement mediated thrombotic microangiopathy in sickle cell disease.
  Haematologica
  07/30/2020 Authors: Chonat S; Graciaa S; Shin HS; Newton JG; Quarmyne M-O; Boudreaux J; Tang A; Zerra PE; Rollins MR; Josephson CD
• VOXELOTOR IN CHILDREN WITH SICKLE CELL ANEMIA: EFFICACY AND IMPROVEMENT IN ERYTHROCYTE PHYSIOLOGY
  Volume: 67 Page(s): S40 - S40
  06/01/2020 Authors: Chonat S; Fields E; Baratz H; Watt A; Pochron M; Dixon S; Tonda M; Lehrer-Graiwer J; Brown C; Archer D
• Genotype-phenotype correlation and molecular heterogeneity in pyruvate kinase deficiency.
  Am J Hematol Volume: 95 Page(s): 472 - 482
  05/01/2020 Authors: Bianchi P; Fermo E; Lezon-Geyda K; van Beers EJ; Morton HD; Barcellini W; Glader B; Chonat S; Ravindranath Y; Newburger PE
• Hemolytic transfusion reactions in sickle cell disease: underappreciated and potentially fatal.
  Haematologica Volume: 105 Page(s): 539 - 544
  03/01/2020 Authors: Thein SL; Pirenne F; Fasano RM; Habibi A; Bartolucci P; Chonat S; Hendrickson JE; Stowell SR
• Fc Gamma Receptors and Complement Component 3 Facilitate Anti-fVIII Antibody Formation.
  Front Immunol Volume: 11 Page(s): 905
  01/01/2020 Authors: Zerra PE; Arthur CM; Chonat S; Maier CL; Mener A; Shin S; Allen JWL; Baldwin WH; Cox C; Verkerke H
• Complement Inhibition in Severe COVID-19 Acute Respiratory Distress Syndrome.
  Front Pediatr Volume: 8 Page(s): 616731
  01/01/2020 Authors: Raghunandan S; Josephson CD; Verkerke H; Linam WM; Ingram TC; Zerra PE; Arthur CM; Stowell SR; Briones M; Chonat S
• Congenital Dyserythropoietic Anemia Type I Due to Biallelic CDAN1 mutations: Report from the Congenital Dyserythropoietic Anemia Registry (CDAR)
  Volume: 134
  11/13/2019 Authors: Niss O; Lorsbach RB; Buchbinder DK; Chonat S; McLemore ML; McCavit T; Schwartz JH; Meznarich J; Seu K; Zhang W
• Examining the Role of Complement in Predicting, Preventing, and Treating Hemolytic Transfusion Reactions.
  Transfus Med Rev Volume: 33 Page(s): 217 - 224
  10/01/2019 Authors: Arthur CM; Chonat S; Fasano R; Yee MEM; Josephson CD; Roback JD; Stowell SR
• MODELING COMPLEMENT-MEDIATED ACUTE LUNG INJURY IN SICKLE CELL MICE
  Volume: 114 Page(s): 496 - 496
  10/01/2019 Authors: Chonat S; Patel S; Jeffers L; Koval M; Archer D; Joiner C; Stowell S
• Complement Mediated Hemolytic Anemia Secondary to Plasmodium ovale Infection in a Child.
  J Pediatr Hematol Oncol Volume: 41 Page(s): 557 - 558
  10/01/2019 Authors: Graciaa S; Russell R; Chonat S
• Mechanisms of Antibody-Mediated RBC Removal: Consequences on Prevention and Treatment
  Volume: 59 Page(s): 13A - 14A
  09/01/2019 Authors: Chonat S; Arthur C; Fuller M; Jajosky R; Zerra P; Maier CL; Stowell S
• EXTRAVASCULAR HEMOLYSIS DURING TREATMENT WITH ECULIZUMAB FOR PAROXYSMAL NOCTURNAL HEMOGLOBINURIA
  Volume: 66
  06/01/2019 Authors: Graciaa S; Chonat S
• Challenges in preventing and treating hemolytic complications associated with red blood cell transfusion.
  Transfus Clin Biol Volume: 26 Page(s): 130 - 134
  05/01/2019 Authors: Chonat S; Arthur CM; Zerra PE; Maier CL; Jajosky RP; Yee MEM; Miller MJ; Josephson CD; Roback JD; Fasano R
• Challenges in the treatment and prevention of delayed hemolytic transfusion reactions with hyperhemolysis in sickle cell disease patients.
  Transfusion Volume: 59 Page(s): 1698 - 1705
  05/01/2019 Authors: Dean CL; Maier CL; Chonat S; Chang A; Carden MA; El Rassi F; McLemore ML; Stowell SR; Fasano RM
• Clinical presentation of delayed hemolytic transfusion reactions and hyperhemolysis in sickle cell disease.
  Transfus Clin Biol Volume: 26 Page(s): 94 - 98
  05/01/2019 Authors: Fasano RM; Miller MJ; Chonat S; Stowell SR
• Chronic Alcohol Significantly Affects Pulmonary Function Both at Baseline and in Response to Endotoxemia
  Volume: 33
  04/01/2019 Authors: Jeffers LA; Smith P; Chonat S; Koval M
• Prevalence and management of iron overload in pyruvate kinase deficiency: report from the Pyruvate Kinase Deficiency Natural History Study.
  Haematologica Volume: 104 Page(s): e51 - e53
  02/01/2019 Authors: van Beers EJ; van Straaten S; Morton DH; Barcellini W; Eber SW; Glader B; Yaish HM; Chonat S; Kwiatkowski JL; Rothman JA
• Corrigendum: The Spectrum of SPTA1-Associated Hereditary Spherocytosis.
  Front Physiol Volume: 10 Page(s): 1331
  01/01/2019 Authors: Chonat S; Risinger M; Sakthivel H; Niss O; Rothman JA; Hsieh L; Chou ST; Kwiatkowski JL; Khandros E; Gorman MF
• EPSTEIN-BARR VIRUS INFECTION OF T AND NK CELLS CAUSES A SEVERE AND UNUSUAL FORM OF HEMOPHAGOCYTIC LYMPHOHITICYTOSIS AMONG HISPANIC PATIENTS
  Volume: 66 Page(s): S42 - S42
  01/01/2019 Authors: Shamriz O; Bunting ST; Briones M; Chonat S; Quarmyne M-O; Chandrakasan S
• The Spectrum of SPTA1-Associated Hereditary Spherocytosis.
  Front Physiol Volume: 10 Page(s): 815
  01/01/2019 Authors: Chonat S; Risinger M; Sakthivel H; Niss O; Rothman JA; Hsieh L; Chou ST; Kwiatkowski JL; Khandros E; Gorman MF
• Complement serves as a switch between CD4+ T cell-independent and -dependent RBC antibody responses.
  JCI Insight Volume: 3
  11/15/2018 Authors: Mener A; Patel SR; Arthur CM; Chonat S; Wieland A; Santhanakrishnan M; Liu J; Maier CL; Jajosky RP; Girard-Pierce K
• Contribution of alternative complement pathway to delayed hemolytic transfusion reaction in sickle cell disease.
  Haematologica Volume: 103 Page(s): e483 - e485
  10/01/2018 Authors: Chonat S; Quarmyne M-O; Bennett CM; Dean CL; Joiner CH; Fasano RM; Stowell SR
• Congenital dyserythropoietic anaemia type I diagnosed in a young adult with a history of splenectomy in childhood for presumed haemolytic anaemia.
  Br J Haematol Volume: 182 Page(s): 10
  07/01/2018 Authors: Chonat S; McLemore ML; Bunting ST; Nortman S; Zhang K; Kalfa TA
• Transfusion-transmitted malaria masquerading as sickle cell crisis with multisystem organ failure.
  Transfusion Volume: 58 Page(s): 1550 - 1554
  06/01/2018 Authors: Maier CL; Gross PJ; Dean CL; Chonat S; Ip A; McLemore M; El Rassi F; Stowell SR; Josephson CD; Fasano RM
• Clinical spectrum of pyruvate kinase deficiency: data from the Pyruvate Kinase Deficiency Natural History Study.
  Blood Volume: 131 Page(s): 2183 - 2192
  05/17/2018 Authors: Grace RF; Bianchi P; van Beers EJ; Eber SW; Glader B; Yaish HM; Despotovic JM; Rothman JA; Sharma M; McNaull MM
• Hereditary xerocytosis: Diagnostic considerations.
  Am J Hematol Volume: 93 Page(s): E67 - E69
  03/01/2018 Authors: Risinger M; Glogowska E; Chonat S; Zhang K; Dagaonkar N; Joiner CH; Quinn CT; Kalfa TA; Gallagher PG
• Alu element insertion in PKLR gene as a novel cause of pyruvate kinase deficiency in Middle Eastern patients.
  Hum Mutat Volume: 39 Page(s): 389 - 393
  03/01/2018 Authors: Lesmana H; Dyer L; Li X; Denton J; Griffiths J; Chonat S; Seu KG; Heeney MM; Zhang K; Hopkin RJ
• Recipient priming to one RBC alloantigen directly enhances subsequent alloimmunization in mice.
  Blood Adv Volume: 2 Page(s): 105 - 115
  01/23/2018 Authors: Patel SR; Bennett A; Girard-Pierce K; Maier CL; Chonat S; Arthur CM; Zerra PE; Mener A; Stowell SR
• Marginal Zone B Cells Induce Alloantibody Formation Following RBC Transfusion.
  Front Immunol Volume: 9 Page(s): 2516
  01/01/2018 Authors: Patel SR; Gibb DR; Girard-Pierce K; Zhou X; Rodrigues LC; Arthur CM; Bennett AL; Jajosky RP; Fuller M; Maier CL
• Extracellular fluid tonicity impacts sickle red blood cell deformability and adhesion.
  Blood Volume: 130 Page(s): 2654 - 2663
  12/14/2017 Authors: Carden MA; Fay ME; Lu X; Mannino RG; Sakurai Y; Ciciliano JC; Hansen CE; Chonat S; Joiner CH; Wood DK
• The First Registry for Patients with Congenital Dyserythropoietic Anemia in North America: Design and Preliminary Results
  Volume: 130
  12/07/2017 Authors: Niss O; Lorsbach RB; Christakopoulos GE; Trump L; Reynolds M; Giger K; Johnson CE; Husami A; Buchbinder DK; Rothman JA
• Primed CD4 T Cells to an Intracellular Alloantigen Facilitate Alloimmunization Following Subsequent Transfusion
  Volume: 130
  12/07/2017 Authors: Patel SR; Bennett AL; Zerra PE; Chonat S; Maier C; Stowell SR
• Current Standards of Care and Long Term Outcomes for Thalassemia and Sickle Cell Disease.
  Volume: 1013 Page(s): 59 - 87
  01/01/2017 Authors: Chonat S; Quinn CT
• Reactive Oxygen Species Produced by NADPH Oxidase Contribute to Cardiac Pathology in a Mouse Model of Sickle Cell Disease
  Volume: 128
  12/02/2016 Authors: Christakopoulos GE; Chonat S; Valiente-Alandi I; Konstantinidis DG; Schleper A; Bakeer N; Loberg A; Blaxall BC; Zheng Y; James J
• Cellular Hydration and Oxidation As Phenotype Modifiers in Sickle Cell Anemia
  Volume: 128
  12/02/2016 Authors: Risinger MA; Dagaonkar N; Christakopoulos GE; Liu J; Seu KG; Konstantinidis DG; Quinn CT; Chonat S; Joiner CH; Zhang K
• Atypical haemolytic uraemic syndrome in a patient with sickle cell disease, successfully treated with eculizumab.
  Br J Haematol Volume: 175 Page(s): 744 - 747
  11/01/2016 Authors: Chonat S; Chandrakasan S; Kalinyak KA; Ingala D; Gruppo R; Kalfa TA
• Genotype-phenotype correlations in hereditary elliptocytosis and hereditary pyropoikilocytosis.
  Blood Cells Mol Dis Volume: 61 Page(s): 4 - 9
  10/01/2016 Authors: Niss O; Chonat S; Dagaonkar N; Almansoori MO; Kerr K; Rogers ZR; McGann PT; Quarmyne M-O; Risinger M; Zhang K
• The Spectrum of Alpha-Spectrin Associated Hereditary Spherocytosis
  Volume: 126
  12/03/2015 Authors: Chonat S; Risinger M; Dagaonkar N; Maghathe T; Rothman J; Connor J; Kalinyak K; Begtrup AH; Zhang K; Kalfa TA
• Alu-Element Insertion in Pklr Gene As a Novel Cause of Severe Hereditary Nonspherocytic Hemolytic Anemia
  Volume: 126
  12/03/2015 Authors: Lesmana H; Dyer L; Zhou P; Li X; Denton J; Chonat S; Zhang K; Hopkin RJ; Kalfa TA
• Complement mutations as disease modifier in paroxysmal nocturnal hemoglobinuria
  Volume: 67 Page(s): 135 - 136
  09/01/2015 Authors: Dixon B; Chonat S; Palumbo J
• Cation Leak in Red Blood Cells of Patients with Wiskott-Aldrich Syndrome Leads to Non-Immunologic Hemolysis
  Volume: 124
  12/06/2014 Authors: Sokolic RA; Chonat S; Risinger M; Eckhaus M; Garabedian E; Calvo KR; Maric I; Kalfa TA; Candotti F
• AUTOSOMAL RECESSIVE HEREDITARY SPHEROCYTOSIS IN PATIENTS WITH THE C.4339-99C> T alpha LEPRA MUTATION IN THE SPTA1 GENE
  PEDIATRIC BLOOD & CANCER Volume: 61 Page(s): S16 - S17
  05/01/2014 Authors: Connor J; Dagaonkar N; Chonat S; Keddache M; Zhang K; Begtrup A; Kalfa T; Dexheimer P
• HEREDITARY SPHEROCYTOSIS DUE TO BIALLELIC OR MONOALLELIC ANKYRIN MUTATIONS
  PEDIATRIC BLOOD & CANCER Volume: 61 Page(s): S70 - S70
  05/01/2014 Authors: Chonat S; Dagaonkar N; Maghathe T; Connor J; Mullins E; Zhang K; Kalfa T
• CHILDHOOD OPTIC NERVE SHEATH MENINGIOMAS
  PEDIATRIC BLOOD & CANCER Volume: 61 Page(s): S70 - S70
  05/01/2014 Authors: Chonat S; Salloum R; Breneman J; Gray M; Koch B; Fouladi M
• ECULIZUMAB TREATMENT OF THROMBOTIC MICROANGIOPATHY (TMA) IN SICKLE CELL DISEASE
  PEDIATRIC BLOOD & CANCER Volume: 61 Page(s): S38 - S38
  05/01/2014 Authors: Chonat S; Chandrakasan S; Kalinyak K; Ingala D; Gruppo R; Kalfa T
• DEVELOPMENT OF A COMPREHENSIVE RAPID NEXT-GENERATION SEQUENCING ASSAY FOR THE DIAGNOSIS OF INHERITED HEMOLYTIC ANEMIA
  PEDIATRIC BLOOD & CANCER Volume: 61 Page(s): S59 - S60
  05/01/2014 Authors: Begtrup AH; Dagaonkar N; Chonat S; Giger K; Husami A; Kissell D; Risinger M; Joiner C; Keddache M; Zhang K
• Absent left common and left external iliac artery presenting in a neonate.
  J Perinatol Volume: 33 Page(s): 407 - 409
  05/01/2013 Authors: Patel M; Chonat S; Olomu I; Arrington S; Kadrofske M
• Cutaneous lesions in transient abnormal myelopoiesis.
  J Paediatr Child Health Volume: 48 Page(s): 184 - 185
  02/01/2012 Authors: Winckworth LC; Chonat S; Uthaya S
• CUTANEOUS LESIONS IN TRANSIENT ABNORMAL MYELOPOIESIS
  JOURNAL OF PAEDIATRICS AND CHILD HEALTH Volume: 48
  02/01/2012 Authors: Winckworth LC; Chonat S; Uthaya S
• Adolescent hematology
  Page(s): 137 - 170
  01/01/2012 Authors: Gera R; Saah EZ; Pawar A; Chonat S; Scott-Emuakpor AB; Kulkarni R
• Co-occurrence of Chiari malformations and sickle cell disease-a diagnostic dilemma: a report of 4 cases and review of literature.
  J Pediatr Hematol Oncol Volume: 33 Page(s): 624 - 625
  12/01/2011 Authors: Chonat S; Saah E; Gera R; Scott-Emuakpor A; Kulkarni R
• Nutritional outcomes in surgical neonates after hospital discharge.
  Pediatr Surg Int Volume: 27 Page(s): 553 - 554
  05/01/2011 Authors: Winckworth LC; Chonat S; Chuang S-L
• NUTRITIONAL OUTCOME OF SURGICAL NEONATES AFTER HOSPITAL DISCHARGE
  PEDIATRIC RESEARCH Volume: 68 Page(s): 533 - 534
  11/01/2010 Authors: Chuang S-L; Winckworth L; Chonat S; Santhoush P; Harley C; Ogundipe E
• WERNICKE'S-LIKE ENCEPHALOPATHY AND GENERALIZED ENCEPHALOPATHY FOLLOWING TREATMENT IN MEDULLOBLASTOMA
  PEDIATRIC BLOOD & CANCER Volume: 54 Page(s): 856 - 856
  06/01/2010 Authors: Chonat S; Saah E; Gera R; Scott-Emuakpor A; Kulkarni R
• NUTRITIONAL FOLLOW-UP IN SURGICAL NEONATES AFTER HOSPITAL DISCHARGE
  JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION Volume: 50 Page(s): E175 - E175
  06/01/2010 Authors: Chuang S; Winckworth L; Chonat S; Harley C; Ogundipe E
• Use of premedication for intubation in tertiary neonatal units in the United Kingdom.
  Paediatr Anaesth Volume: 19 Page(s): 653 - 658
  07/01/2009 Authors: Chaudhary R; Chonat S; Gowda H; Clarke P; Curley A
• A rare case of fatal infantile juvenile systemic xanthogranuloma
  Volume: 159 Page(s): 120 - 121
  07/01/2008 Authors: Hafiji J; Wimalendra M; Chonat S; Hook E; Burke A; Burrows NP
• Use of pre-medication before intubation in tertiary neonatal units in the United Kingdom
  ACTA PAEDIATRICA Volume: 96 Page(s): 98 - 98
  10/01/2007 Authors: Chonat S; Chaudhary R; Gowda H; Clarke P; Curley A
• Variations in practice among paediatric consultants when referring unexpected neonatal deaths to a coroner.
  Arch Dis Child Fetal Neonatal Ed Volume: 92 Page(s): F234
  05/01/2007 Authors: Chonat S; Lakshman R; Clements M; Iles R