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Profile

Jeong Hong

  • Department of Pediatrics
    Associate Professor
  • (404) 727-3519
  • jeong.s.hong@emory.edu
Head shot of Jeong Hong

Research

Publications

  • Evaluating elexacaftor/tezacaftor/ivacaftor (ETI; Trikafta) for treatment of patients with non-cystic fibrosis bronchiectasis (NCFBE): A clinical study protocol.
    PLoS One Volume: 20 Page(s): e0316721
    01/01/2025 Authors: Swenson CE; Hunt WR; Manfredi C; Beltran DJ; Hong JS; Davis BR; Suzuki S; Barill C; Rab A; Chico C
  • Evaluation of elexacaftor-tezacaftor-ivacaftor treatment in individuals with cystic fibrosis and CFTRN1303K in the USA: a prospective, multicentre, open-label, single-arm trial.
    Lancet Respir Med Volume: 12 Page(s): 947 - 957
    12/01/2024 Authors: Solomon GM; Linnemann RW; Rich R; Streby A; Buehler B; Hunter E; Vijaykumar K; Hunt WR; Brewington JJ; Rab A
  • Translation velocity determines the efficacy of engineered suppressor tRNAs on pathogenic nonsense mutations.
    Nat Commun Volume: 15 Page(s): 2957
    04/05/2024 Authors: Bharti N; Santos L; Davyt M; Behrmann S; Eichholtz M; Jimenez-Sanchez A; Hong JS; Rab A; Sorscher EJ; Albers S
  • Mutation accumulation in H. sapiens F508del CFTR countermands dN/dS type genomic analysis.
    PLoS One Volume: 19 Page(s): e0305832
    01/01/2024 Authors: Hong JS; Tindall JM; Tindall SR; Sorscher EJ
  • In silico analysis and theratyping of an ultra-rare CFTR genotype (W57G/A234D) in primary human rectal and nasal epithelial cells.
    iScience Volume: 26 Page(s): 108180
    11/17/2023 Authors: Kleinfelder K; Lotti V; Eramo A; Amato F; Lo Cicero S; Castelli G; Spadaro F; Farinazzo A; Dell'Orco D; Preato S
  • Mechanisms by which the cystic fibrosis transmembrane conductance regulator may influence SARS-CoV-2 infection and COVID-19 disease severity.
    FASEB J Volume: 37 Page(s): e23220
    11/01/2023 Authors: Tedbury PR; Manfredi C; Degenhardt F; Conway J; Horwath MC; McCracken C; Sorscher AJ; Moreau S; Wright C; Edwards C
  • A Novel 7H-[1,2,4]Triazolo[3,4-b]thiadiazine-based Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Directed toward Treatment of Cystic Fibrosis.
    ACS Med Chem Lett Volume: 14 Page(s): 1338 - 1343
    10/12/2023 Authors: Rab A; Yang X; Tracy WF; Hong JS; Joshi D; Manfredi C; Ponnaluri SS; Kolykhalov AA; Qui M; Fu H
  • Elexacaftor/VX-445-mediated CFTR interactome remodeling reveals differential correction driven by mutation-specific translational dynamics.
    J Biol Chem Volume: 299 Page(s): 105242
    10/01/2023 Authors: Kim M; McDonald EF; Sabusap CMP; Timalsina B; Joshi D; Hong JS; Rab A; Sorscher EJ; Plate L
  • Engineered tRNAs suppress nonsense mutations in cells and in vivo.
    Nature Volume: 618 Page(s): 842 - 848
    06/01/2023 Authors: Albers S; Allen EC; Bharti N; Davyt M; Joshi D; Perez-Garcia CG; Santos L; Mukthavaram R; Delgado-Toscano MA; Molina B
  • High-throughput screens identify a lipid nanoparticle that preferentially delivers mRNA to human tumors in vivo.
    J Control Release Volume: 357 Page(s): 394 - 403
    05/01/2023 Authors: Huayamares SG; Lokugamage MP; Rab R; Da Silva Sanchez AJ; Kim H; Radmand A; Loughrey D; Lian L; Hou Y; Achyut BR
  • Elexacaftor/VX-445-mediated CFTR interactome remodeling reveals differential correction driven by mutation-specific translational dynamics.
    bioRxiv
    02/04/2023 Authors: Kim M; McDonald EF; Sabusap CMP; Timalsina B; Joshi D; Hong JS; Rab A; Sorscher EJ; Plate L
  • Antisense oligonucleotide-based drug development for Cystic Fibrosis patients carrying the 3849+10kb C-to-T splicing mutation.
    J Cyst Fibros Volume: 20 Page(s): 865 - 875
    09/01/2021 Authors: Oren YS; Irony-Tur Sinai M; Golec A; Barchad-Avitzur O; Mutyam V; Li Y; Hong J; Ozeri-Galai E; Hatton A; Leibson C
  • A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion.
    Nat Commun Volume: 12 Page(s): 4358
    07/16/2021 Authors: Sharma J; Du M; Wong E; Mutyam V; Li Y; Chen J; Wangen J; Thrasher K; Fu L; Peng N
  • Stability Prediction for Mutations in the Cytosolic Domains of Cystic Fibrosis Transmembrane Conductance Regulator.
    J Chem Inf Model Volume: 61 Page(s): 1762 - 1777
    04/26/2021 Authors: Bahia MS; Khazanov N; Zhou Q; Yang Z; Wang C; Hong JS; Rab A; Sorscher EJ; Brouillette CG; Hunt JF
  • The CFTR P67L variant reveals a key role for N-terminal lasso helices in channel folding, maturation, and pharmacologic rescue.
    J Biol Chem Volume: 296 Page(s): 100598
    01/01/2021 Authors: Sabusap CM; Joshi D; Simhaev L; Oliver KE; Senderowitz H; van Willigen M; Braakman I; Rab A; Sorscher EJ; Hong JS
  • Ivacaftor Reverses Airway Mucus Abnormalities in a Rat Model Harboring a Humanized G551D-CFTR.
    Am J Respir Crit Care Med Volume: 202 Page(s): 1271 - 1282
    11/01/2020 Authors: Birket SE; Davis JM; Fernandez-Petty CM; Henderson AG; Oden AM; Tang L; Wen H; Hong J; Fu L; Chambers A
  • G551D mutation impairs PKA-dependent activation of CFTR channel that can be restored by novel GOF mutations.
    Am J Physiol Lung Cell Mol Physiol Volume: 319 Page(s): L770 - L785
    11/01/2020 Authors: Wang W; Fu L; Liu Z; Wen H; Rab A; Hong JS; Kirk KL; Rowe SM
  • IPS-DERIVED AIRWAY CELL RESPONSE TO CFTR MODULATION: STUDY OF TRIPLE COMBINATION THERAPY IN CF PATIENTS WITHOUT AN APPROVED MODULATOR
    Volume: 55 Page(s): S207 - S207
    10/01/2020 Authors: Linnemann RW; Streby A; Rab A; Solomon GM; Hunter E; Hailemichael T; Driggers WC; Slaten K; Hathorne H; Hong JS
  • IMPROVED FUNCTIONAL RESCUE OF G551D CFTR BY TRIPLE COMBINATION THERAPY
    Volume: 55 Page(s): S188 - S189
    10/01/2020 Authors: Rab A; Suzuki S; Disha J; Barilla C; Goller K; Manfredi C; Flores JK; Streby A; Stecenko A; Feldman RJ
  • APPLICATION OF IPSC-DERIVED AIRWAY EPITHELIUM FOR EVALUATING THE RESPONSE OF RARE OR UNKNOWN CFTR MUTATIONS TO MODULATORS
    Volume: 55 Page(s): S193 - S193
    10/01/2020 Authors: Barilla C; Suzuki S; Rab A; Goller K; Hong JS; Driggers WC; Flores J; Feldman RJ; Solomon GM; Stecenko A
  • CYSTIC FIBROSIS CARRIER STATUS AND PULMONARY TUBERCULOSIS IN THE TBILISI, GEORGIA REGIONS OF EUROPE
    Volume: 55 Page(s): S115 - S115
    10/01/2020 Authors: Hong JS; Ziegler TR; Figueroa J; Alvarez JA; Tangpricha V; Tukvadze N; Blumberg HM; McCracken C; Sorscher EJ
  • UTILIZING YEAST PHENOMICS TO DISCOVER GENE INTERACTION NETWORKS THAT INFLUENCE BIOGENESIS OF CFTR NONSENSE ALLELES
    Volume: 55 Page(s): S118 - S119
    10/01/2020 Authors: Oliver KE; Mao Y; Laflin S; Linscott K; Gaines E; Ali H; Hong JS; Rab A; Sorscher EJ; Hartman JL
  • DEFINING MODULATOR RESPONSE IN A SUBJECT WITH N1303K/G27V CFTR THROUGH MULTIPLE MODEL SYSTEMS
    Volume: 55 Page(s): S185 - S185
    10/01/2020 Authors: Hong JS; Manfredi C; Hadjiliadis D; Ostmann A; O'Shaughnessy RA; Strecker LM; Moncivaiz JD; Sorscher EJ; Brewington JJ
  • The use of Trichomonas vaginalis purine nucleoside phosphorylase to activate fludarabine in the treatment of solid tumors.
    Cancer Chemother Pharmacol Volume: 85 Page(s): 573 - 583
    03/01/2020 Authors: Parker WB; Allan PW; Waud WR; Hong J; Gilbert-Ross M; Achyut BR; Joshi D; Behbahani T; Rab R; Ealick SE
  • Slowing ribosome velocity restores folding and function of mutant CFTR.
    J Clin Invest Volume: 129 Page(s): 5236 - 5253
    12/02/2019 Authors: Oliver KE; Rauscher R; Mijnders M; Wang W; Wolpert MJ; Maya J; Sabusap CM; Kesterson RA; Kirk KL; Rab A
  • An Ancient CFTR Ortholog Informs Molecular Evolution in ABC Transporters.
    Dev Cell Volume: 51 Page(s): 421 - 430.e3
    11/18/2019 Authors: Cui G; Hong J; Chung-Davidson Y-W; Infield D; Xu X; Li J; Simhaev L; Khazanov N; Stauffer B; Imhoff B
  • Cystic fibrosis precision therapeutics: Emerging considerations.
    Pediatr Pulmonol Volume: 54 Suppl 3 Page(s): S13 - S17
    11/01/2019 Authors: Joshi D; Ehrhardt A; Hong JS; Sorscher EJ
  • COMBINATION TRANSLATIONAL READTHROUGH THERAPY TO POTENTIATE SUPPRESSION OF CYSTIC FIBROSIS PREMATURE TERMINATION CODON MUTATIONS
    Volume: 54 Page(s): S349 - S349
    10/01/2019 Authors: Sharma J; Mutyam V; Du M; Li Y; Chen J; Hong JS; Bostwick B; Augelli-Szafran C; Coote K; Liang F
  • LAMPREY CFTR: AN ANCIENT CFTR ORTHOLOG INFORMS MOLECULAR EVOLUTION IN ABC TRANSPORTERS
    Volume: 54 Page(s): S195 - S195
    10/01/2019 Authors: Cui G; Hong JS; Chung-Davidson Y; Infield D; Xu X; Simhaev L; Khazanov N; Stauffer BB; Imhoff B; Cottrill KA
  • CFTR MRNA EXPRESSION ANALYSIS UTILIZING A REPOSITORY OF BANKED PRIMARY AIRWAY EPITHELIAL SAMPLES
    Volume: 54 Page(s): S248 - S248
    10/01/2019 Authors: Manfredi C; Rab A; Sorscher EJ; Hong JS
  • GENE EDITING OF W1282X CFTR ONTO A NATIVE GENETIC BACKGROUND, AND IMPLICATIONS FOR IONOCYTE-DEPENDENT TRANSEPITHELIAL TRANSPORT
    Volume: 54 Page(s): S216 - S216
    10/01/2019 Authors: Rab A; Waller L; Gustin J; Manfredi C; Disha J; Lipman C; Hong JS; Sorscher EJ
  • PROTEOSTASIS PROFILING OF CLASS II CFTR MUTATIONS AS A MECHANISM FOR PREDICTING LUMACAFTOR THERATYPE
    Volume: 54 Page(s): S199 - S199
    10/01/2019 Authors: Sabusap CP; McDonald E; Hong JS; Sorscher EJ; Plate L
  • PARTIAL RESCUE OF G542X-AND W1282X-CFTR IS ACHIEVED FOLLOWING SUPPRESSION OF SPECIFIC RIBOSOMAL COMPONENTS
    Volume: 54 Page(s): S199 - S200
    10/01/2019 Authors: Oliver KE; Ali H; Rauscher R; Bampi GB; Santos S; Rab A; Hong JS; Ignatova Z; Sorscher EJ; Hartman JL
  • G551D-CFTR IS DEFECTIVE IN CHANNEL PHOSPHORYLATION THAT CAN BE RESTORED BY GAIN-OF-FUNCTION MUTATIONS
    Volume: 54 Page(s): S185 - S185
    10/01/2019 Authors: Wang W; Fu LK; Liu Z; Wen H; Hong JS; Kirk KL; Rowe S
  • VX-770-mediated potentiation of numerous human CFTR disease mutants is influenced by phosphorylation level.
    Sci Rep Volume: 9 Page(s): 13460
    09/17/2019 Authors: Cui G; Stauffer BB; Imhoff BR; Rab A; Hong JS; Sorscher EJ; McCarty NA
  • Making precision medicine personal for cystic fibrosis.
    Science Volume: 365 Page(s): 220 - 221
    07/19/2019 Authors: Manfredi C; Tindall JM; Hong JS; Sorscher EJ
  • Non-obstructive vas deferens and epididymis loss in cystic fibrosis rats.
    Mech Dev Volume: 155 Page(s): 15 - 26
    02/01/2019 Authors: Plyler ZE; Birket SE; Schultz BD; Hong JS; Rowe SM; Petty CF; Crowley MR; Crossman DK; Schoeb TR; Sorscher EJ
  • SUPPRESSION OF PEROXISOME AND RIBOSOMAL CONSTITUENTS PARTIALLY RESTORES PLASMA MEMBRANE LOCALIZATION AND FUNCTION OF W1282X-CFTR
    Volume: 53 Page(s): 209 - 210
    09/01/2018 Authors: Ali H; Icyuz M; Kelly S; Rab A; Hong JS; Bedwell D; Hartman JL; Sorscher EJ; Oliver KE
  • CFTR PHOSPHORYLATION LEVEL MODULATES THE EFFICACY OF VX-770-MEDIATED POTENTIATION OF NUMEROUS HUMAN CFTR DISEASE-ASSOCIATED VARIANTS
    Volume: 53 Page(s): 110 - 111
    09/01/2018 Authors: Cui G; Stauffer BB; Imhoff B; Rab A; Hong JS; Sorscher EJ; McCarty NA
  • EVALUATION OF W1282X CFTR IN THE FRT MODEL AS A MEANS TO TEST SMALL MOLECULE INTERVENTIONS
    Volume: 53 Page(s): 213 - 213
    09/01/2018 Authors: Manfredi C; Rab A; Hong JS; Joshi D; Mahiou J; Mense M; Sorscher EJ
  • EXAMPLES OF CFTR "SUPER-RESPONDERS," AS WELL AS VARIANTS WITH NEGLIGIBLE ACTIVITY AND MINIMAL PHARMACOLOGIC CORRECTION
    Volume: 53 Page(s): 168 - 168
    09/01/2018 Authors: Rab A; Joshi D; Oliver KE; Sorseher EJ; Hong JS
  • STRUCTURE OF CFTR N-TERMINAL LASSO HELICES AS A GUIDE FOR EVALUATING MUTANT CFTR CHANNEL FOLDING, MATURATION, AND PHARMACOLOGIC RESCUE
    Volume: 53 Page(s): 152 - 152
    09/01/2018 Authors: Sabusap CP; Joshi D; Rab A; Solomon GM; Simhaev L; Sorscher EJ; Senderowitz H; Hong JS
  • THERATYPING RARE AND COMMON CFTR MISSENSE VARIANTS BASED ON RESIDUAL FUNCTION AND PHENOTYPE
    Volume: 53 Page(s): 262 - 263
    09/01/2018 Authors: Raraigh KS; Han ST; Rab A; Matthew P; Evans TA; Davis E; McCague A; Joynt A; Lu Z; Sharma N
  • RIBOSOMAL PROTEIN L12 IS A MOLECULAR TARGET SUITABLE FOR RESCUE OF CFTR DEFECTS WITH MULTIPLE DISEASE SUBCATEGORIES
    Volume: 53 Page(s): 148 - 148
    09/01/2018 Authors: Oliver KE; Rauscher R; Ali H; Icyuz M; Rab A; Hong JS; Hartman JL; Ignatova Z; Sorscher EJ
  • Residual function of cystic fibrosis mutants predicts response to small molecule CFTR modulators.
    JCI Insight Volume: 3
    07/26/2018 Authors: Han ST; Rab A; Pellicore MJ; Davis EF; McCague AF; Evans TA; Joynt AT; Lu Z; Cai Z; Raraigh KS
  • A HUMANIZED G551D RAT MODEL TO EVALUATE CF AIRWAY DISEASE
    Volume: 52 Page(s): S274 - S274
    09/01/2017 Authors: Birket S; Davis JM; Oden AM; Hong JS; Tearney G; Sorscher EJ; Rowe SM
  • SLOWING TRANSLATION STABILIZES CFTR TRANSMEMBRANE DOMAINS, INCREASES OPEN CHANNEL PROBABILITY AND ENHANCES FOLDING IN VIVO
    Volume: 52 Page(s): S220 - S220
    09/01/2017 Authors: Oliver KE; Rauscher R; Mijnders M; Wang W; Maya J; Kirk KL; Kesterson RA; Hong JS; Braakman I; Hartman JL
  • THERAPY-BASED CLASSIFICATION OF RARE CFTR MUTATIONS
    Volume: 52 Page(s): S330 - S330
    09/01/2017 Authors: Rab A; Manfredi C; Joshi D; Sorscher EJ; Hong JS
  • LAMPREY CFTR, AN EVOLUTIONARY ANCESTOR OF HUMAN CFTR, EXHIBITS NUMEROUS BIOPHYSICAL DISSIMILARITIES FROM HUMAN CFTR
    Volume: 52 Page(s): S224 - S224
    09/01/2017 Authors: Cui G; Hong JS; Stauffer B; Imhoff BR; Gaggar A; McCarty NA
  • NON-OBSTRUCTIVE LOSS OF MALE REPRODUCTIVE TRACT IN CYSTIC FIBROSIS RATS
    Volume: 52 Page(s): S280 - S280
    09/01/2017 Authors: Plyler ZE; Schoeb TR; Hong JS; Rowe SM; Schultz B; Birket S; Sorscher EJ
  • G551D-CFTR HAS GREATLY REDUCED PKA SENSITIVITY THAT CAN BE RESTORED BY NOVEL GAIN-OF-FUNCTION MUTATIONS
    Volume: 52 Page(s): S221 - S221
    09/01/2017 Authors: Wang W; Liu Z; Hong JS; Kirk KL
  • CFTR2 MUTATIONS IN NBD1: CORRELATION BETWEEN IN VITRO THERMAL INSTABILITY AND SEVERITY OF FOLDING DEFECT
    Volume: 52 Page(s): S235 - S235
    09/01/2017 Authors: Yang Z; Zhou Q; Rab A; Hong JS; Khazanov N; Senderowitz H; Sorscher EJ
  • MODULATOR RESPONSIVENESS OF CFTR VARIANTS ASSOCIATED WITH REPLACEMENT AT THE SAME POSITION BY DISTINCT AMINO ACIDS: S549N AND S549R
    Volume: 52 Page(s): S234 - S234
    09/01/2017 Authors: Rab A; Al-Salmani M; Hong JS; Cai Z; Fass UW; Sorscher EJ; Sheppard DN
  • IDENTIFICATION AND PROFILING OF SMALL MOLECULES DISPLAYING CFTR FUNCTIONAL RESCUE ACTIVITY IN FRT CELLS STABLY TRANSFECTED WITH Y122X, G542X, OR W1282X cDNA
    Volume: 52 Page(s): S328 - S328
    09/01/2017 Authors: Bihler H; Harrington J; Musisi I; Cheng Y; Mercadante D; Hong JS; Rab A; Sorscher EJ; Saltz J; Mahiou J
  • THE P67L CFTR BIOGENESIS DEFECT AND ROLE OF N-TERMINAL LASSO HELICES THAT IMPACT CFTR FOLDING AND MATURATION
    Volume: 52 Page(s): S232 - S232
    09/01/2017 Authors: Sabusap CP; Rab A; Oliver KE; Hong J; Sorscher EJ
  • MOLECULAR STUDIES AND DRUG DEVELOPMENT FOR THE CFTR W1282X VARIANT
    Volume: 52 Page(s): S327 - S327
    09/01/2017 Authors: Manfredi C; Rab A; Molina SA; Joshi D; Hong J; Ehrhardt A; Sorscher EJ
  • Discovery of Clinically Approved Agents That Promote Suppression of Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations.
    Am J Respir Crit Care Med Volume: 194 Page(s): 1092 - 1103
    11/01/2016 Authors: Mutyam V; Du M; Xue X; Keeling KM; White EL; Bostwick JR; Rasmussen L; Liu B; Mazur M; Hong JS
  • COMBINATIONS OF TRAFFICKING/FOLDING CORRECTORS AND READTHROUGH MODULATORS AS THERAPEUTIC APPROACH FOR CFTR PTC MUTATIONS
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 208 - 209
    10/01/2016 Authors: Liang F; Wong E; Jordan NJ; Haibo S; Fitzpatrick LM; Hong JS; Rab A; Sorscher EJ; Mense M
  • HIGH-THROUGHPUT SCREENING FOR READTHROUGH MODULATORS OF CFTR PTC MUTATIONS Y122X AND W1282X
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 293 - 293
    10/01/2016 Authors: Haibo S; Wong E; Jordan NJ; Fitzpatrick LM; Hong JS; Rab A; Sorscher EJ; Liang F; Mense M
  • MOLECULAR ANALYSIS OF THE CFTR W1282X MUTATION
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 293 - 294
    10/01/2016 Authors: Manfredi C; Rab A; Joshi D; Wang W; Kirk K; Saltz J; Mense M; Mahiou J; Sorscher EJ; Hong JS
  • MODEL SYSTEMS FOR INVESTIGATING MOLECULAR PATHOGENESIS OF RARE CFTR ALLELES
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 256 - 257
    10/01/2016 Authors: Rab A; Wen H; Manfredi C; Ehrhardt A; Joshi D; Sorscher EJ; Hong JS
  • FUNCTIONAL CHARACTERIZATION OF ESTABLISHED AND NOVEL NONSENSE MUTATION READTHROUGH MODULATORS IN ENGINEERED FRT CELL LINES AND PRIMARY HUMAN BRONCHIAL EPITHELIAL (HBE) CELLS
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 264 - 264
    10/01/2016 Authors: Bihler H; Harrington J; Musisi I; Mercadante D; Hong JS; Rab A; Sorscher EJ; Saltz J; Mahiou J; Wong E
  • RIBOSOMAL TARGETING CORRECTS CFTR CLASS I AND II DEFECTS
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 209 - 209
    10/01/2016 Authors: Oliver KE; Wang W; Wolpert MJ; Maya J; Icyuz M; Hong JS; Hartman JL; Sorscher EJ
  • ESCIN, A POTENTIAL READTHROUGH AGENT THAT PROMOTES SUPPRESSION OF CFTR PREMATURE TERMINATION CODON MUTATIONS
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 266 - 267
    10/01/2016 Authors: Sharma J; Mutyam V; Peng N; Hong JS; Mense M; E Augelli-Szafran C; Pathak V; J. Suto M; Bostwick R; Bedwell DM
  • CHARACTERIZATION OF P67L CFTR AS A MODEL OF "PRECISION" THERAPEUTICS FOR RARE CFTR ALLELES
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 196 - 196
    10/01/2016 Authors: Sabusap CP; Fu L; McNicholas-Bevensee CM; Wang W; Chung W; Wen H; Mazur M; Kirk K; Collawn JF; Hong JS
  • ANALYSIS OF VAS DEFERENS ATRESIA IN THE CF RAT
    PEDIATRIC PULMONOLOGY Volume: 51 Page(s): 256 - 256
    10/01/2016 Authors: Plyler ZE; Schoeb TR; Hong JS; Tuggle KL; Birket S; Schultz BD; Sorscher EJ
  • Analysis of cystic fibrosis-associated P67L CFTR illustrates barriers to personalized therapeutics for orphan diseases.
    JCI Insight Volume: 1
    09/08/2016 Authors: Sabusap CM; Wang W; McNicholas CM; Chung WJ; Fu L; Wen H; Mazur M; Kirk KL; Collawn JF; Hong JS
  • From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations.
    Mol Biol Cell Volume: 27 Page(s): 424 - 433
    02/01/2016 Authors: Veit G; Avramescu RG; Chiang AN; Houck SA; Cai Z; Peters KW; Hong JS; Pollard HB; Guggino WB; Balch WE
  • Channel Gating Regulation by the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) First Cytosolic Loop.
    J Biol Chem Volume: 291 Page(s): 1854 - 1865
    01/22/2016 Authors: Ehrhardt A; Chung WJ; Pyle LC; Wang W; Nowotarski K; Mulvihill CM; Ramjeesingh M; Hong J; Velu SE; Lewis HA
  • Robust Stimulation of W1282X-CFTR Channel Activity by a Combination of Allosteric Modulators.
    PLoS One Volume: 11 Page(s): e0152232
    01/01/2016 Authors: Wang W; Hong JS; Rab A; Sorscher EJ; Kirk KL
  • Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics.
    PLoS One Volume: 11 Page(s): e0163615
    01/01/2016 Authors: Chung WJ; Goeckeler-Fried JL; Havasi V; Chiang A; Rowe SM; Plyler ZE; Hong JS; Mazur M; Piazza GA; Keeton AB
  • PRE-CLINICAL AND CLINICAL VALIDATION OF AN ANTI-CANCER MODALITY THAT ABLATES REFRACTORY, LOW GROWTH FRACTION TUMORS.
    Trans Am Clin Climatol Assoc Volume: 127 Page(s): 59 - 70
    01/01/2016 Authors: Sorscher EJ; Hong JS; Parker WB
  • ANALYSIS OF P67L CFTR ILLUSTRATES BARRIERS TO THERAPEUTIC DEVELOPMENT FOR RARE CF MUTATIONS
    PEDIATRIC PULMONOLOGY Volume: 50 Page(s): 279 - 279
    10/01/2015 Authors: Sabusap CP; Fu L; McNicholas-Bevensee C; Wang W; Chung W; Wen H; Mazur M; Kirk K; Collawn J; Hong JS
  • ANALYSIS OF THE EFFECTS OF RARE CYSTIC FIBROSIS MUTATIONS ON CFTR EXPRESSION, STABILITY AND FUNCTION
    PEDIATRIC PULMONOLOGY Volume: 50 Page(s): 193 - 194
    10/01/2015 Authors: Cai Z; Millen L; Gottschalk LB; Cutting GR; Hong JS; Lukacs GL; Sheppard DN; Sorscher EJ; Thomas PJ; Tuggle KL
  • TARGETING THE RIBOSOME AS A NOVEL APPROACH TO CORRECTING CFTR CLASS II TRAFFICKING DEFECTS
    PEDIATRIC PULMONOLOGY Volume: 50 Page(s): 197 - 197
    10/01/2015 Authors: Oliver KE; Veit G; Wolpert M; Guo J; Icyuz M; Hong JS; Wen H; Sorscher EJ; Lukacs GL; Schneider DA
  • EPITHELIAL CELL MODELS EXPRESSING DIVERSE CFTR MUTATIONS FOR STUDIES OF DISEASE MECHANISM AND DRUG DISCOVERY
    PEDIATRIC PULMONOLOGY Volume: 50 Page(s): 259 - 259
    10/01/2015 Authors: Rab A; Hong JS; Wen H; Sorscher EJ
  • DISTINCT PREMATURE TERMINATION CODON MUTATIONS OF CFTR MAY BENEFIT FROM SPECIFIC THERAPEUTIC APPROACHES TO CORRECTION AND READ-THROUGH MODULATION
    PEDIATRIC PULMONOLOGY Volume: 50 Page(s): 202 - 202
    10/01/2015 Authors: Liang F; Jordan NJ; Shang H; Wong E; Schneider C; Hong JS; Rab A; Sorscher EJ; Bihler H; Mense M
  • Phase I dose-escalating trial of Escherichia coli purine nucleoside phosphorylase and fludarabine gene therapy for advanced solid tumors.
    Ann Oncol Volume: 26 Page(s): 1481 - 1487
    07/01/2015 Authors: Rosenthal EL; Chung TK; Parker WB; Allan PW; Clemons L; Lowman D; Hong J; Hunt FR; Richman J; Conry RM
  • First-in-human dose-escalating trial of E. coli purine nucleoside phosphorylase and fludarabine gene therapy for advanced solid tumors.
    Volume: 33
    05/20/2015 Authors: Chung TK; Rosenthal E; Parker WB; Allan P; Clemons L; Lowman D; Hong J; Hunt FR; Richman J; Conry RM
  • EPITHELIAL MODELS ENCODING DIVERSE CFTR2 MUTATIONS FOR STUDIES OF DISEASE MECHANISM AND DRUG DISCOVERY
    PEDIATRIC PULMONOLOGY Volume: 49 Page(s): 277 - 278
    09/01/2014 Authors: Hong JS; Mahiou J; Liang F; Bihler HJ; Mense M; Lukacs GL; Wen H; Sorscher EJ
  • FUNCTIONAL CLASSIFICATION OF CFTR CORRECTORS BY PARALLEL TESTING IN TWO ISOGENIC FRT CELL LINES EXPRESSING CFTR F508DEL PROTEIN WITH SPECIFIC SUPPRESSOR MUTATIONS
    PEDIATRIC PULMONOLOGY Volume: 49 Page(s): 237 - 237
    09/01/2014 Authors: Finegan JF; Harrington JM; Musisi I; Bihler HJ; Wong E; Liang F; Hong JS; Sorscher EJ; Mense M
  • DEFINING ALLELIC HETEROGENEITY AMONG CLINICALLY IMPORTANT MUTATIONS IN CFTR
    PEDIATRIC PULMONOLOGY Volume: 49 Page(s): 275 - 276
    09/01/2014 Authors: Hong JS; Sorscher EJ; Plyler ZE; Keiles S
  • MODULATING THE DYNAMICS OF RIBOSOME FUNCTION RESCUES F508DEL CFTR MATURATIONAL ARREST
    PEDIATRIC PULMONOLOGY Volume: 49 Page(s): 217 - 217
    09/01/2014 Authors: Oliver KE; Veit G; Icyuz M; Guo J; McClure ML; Hong JS; Wen H; Sorscher EJ; Lukacs GL; Hartman JL
  • IMPACT OF PALMITOYLATION ON CLINICALLY SIGNIFICANT MUTATIONS CHARACTERIZED BY CFTR2
    PEDIATRIC PULMONOLOGY Volume: 49 Page(s): 241 - 242
    09/01/2014 Authors: Sabusap C; Hong JS; McClure M; Chung W; Wen H; Sorscher EJ
  • Intranasal adenovirus-vectored vaccine for induction of long-lasting humoral immunity-mediated broad protection against influenza in mice.
    J Virol Volume: 88 Page(s): 9693 - 9703
    09/01/2014 Authors: Kim EH; Park H-J; Han G-Y; Song M-K; Pereboev A; Hong JS; Chang J; Byun Y-H; Seong BL; Nguyen HH
  • S-palmitoylation regulates biogenesis of core glycosylated wild-type and F508del CFTR in a post-ER compartment.
    Biochem J Volume: 459 Page(s): 417 - 425
    04/15/2014 Authors: McClure ML; Wen H; Fortenberry J; Hong JS; Sorscher EJ
  • Synthetic aminoglycosides efficiently suppress cystic fibrosis transmembrane conductance regulator nonsense mutations and are enhanced by ivacaftor.
    Am J Respir Cell Mol Biol Volume: 50 Page(s): 805 - 816
    04/01/2014 Authors: Xue X; Mutyam V; Tang L; Biswas S; Du M; Jackson LA; Dai Y; Belakhov V; Shalev M; Chen F
  • Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats.
    PLoS One Volume: 9 Page(s): e91253
    01/01/2014 Authors: Tuggle KL; Birket SE; Cui X; Hong J; Warren J; Reid L; Chambers A; Ji D; Gamber K; Chu KK
  • S-PALMITOYLATION REGULATES STABILITY OF CORE GLYCOSYLATED WILD-TYPE AND F508DEL CFTR IN A POST-ER COMPARTMENT
    PEDIATRIC PULMONOLOGY Volume: 48 Page(s): 221 - 221
    10/01/2013 Authors: McClure M; Hong JS; Wen H; Sorscher EJ
  • CHARACTERIZATION OF THE CFTR-KNOCKOUT RAT
    PEDIATRIC PULMONOLOGY Volume: 48 Page(s): 271 - 271
    10/01/2013 Authors: Tuggle KL; Birket S; Fortenberry J; Du M; Tang L; Hong J; Bedwell DM; Rowe SM; Sorscher EJ; Fanucchi M
  • DERIVATION AND CHARACTERIZATION OF A CFTR EXPRESSING CELL LINE AMENABLE FOR ION TRANSPORT STUDIES
    PEDIATRIC PULMONOLOGY Volume: 48 Page(s): 277 - 277
    10/01/2013 Authors: Jackson L; Tang L; Wen H; Bridges RJ; Sorscher EJ; Rowe SM; Hong JS
  • CONSTITUTIVE EXPRESSION OF CFTR SUPPRESSOR MUTATIONS AS A TOOL FOR INVESTIGATING F508DEL CORRECTION
    PEDIATRIC PULMONOLOGY Volume: 48 Page(s): 274 - 274
    10/01/2013 Authors: Hong JS; Tuggle KL; Wen H; Sorscher EJ
  • Respiratory syncytial virus infection disrupts monolayer integrity and function in cystic fibrosis airway cells.
    Viruses Volume: 5 Page(s): 2260 - 2271
    09/19/2013 Authors: Kong M; Maeng P; Hong J; Szczesniak R; Sorscher E; Sullender W; Clancy JP
  • A yeast phenomic model for the gene interaction network modulating CFTR-F508 protein biogenesis.
    Genome Med Volume: 4 Page(s): 103
    12/27/2012 Authors: Louie RJ; Guo J; Rodgers JW; White R; Shah N; Pagant S; Kim P; Livstone M; Dolinski K; McKinney BA
  • POST-TRANSLATIONAL MODIFICATIONS OF CFTR GLYCOFORMS IDENTIFIED BY HIGH RESOLUTION, HIGH MASS ACCURACY MASS SPECTROMETRY
    PEDIATRIC PULMONOLOGY Volume: 47 Page(s): 246 - 246
    09/01/2012 Authors: McClure M; Wilson L; Ray M; DeLucas LJ; Rowe S; Wu X; Dai Q; Hong J; Sorscher EJ; Kappes JC
  • S-PALMITOYLATION MEDIATES TRAFFICKING OF CFTR TO THE CELL SURFACE
    PEDIATRIC PULMONOLOGY Volume: 47 Page(s): 246 - 246
    09/01/2012 Authors: McClure M; Wilson L; Ray M; DeLucas LJ; Rowe S; Wu X; Dai Q; Hong JS; Kappes JC; Barnes S
  • In vivo antitumor activity of intratumoral fludarabine phosphate in refractory tumors expressing E. coli purine nucleoside phosphorylase.
    Cancer Chemother Pharmacol Volume: 70 Page(s): 321 - 329
    08/01/2012 Authors: Sorscher EJ; Hong JS; Allan PW; Waud WR; Parker WB
  • Purification of CFTR for mass spectrometry analysis: identification of palmitoylation and other post-translational modifications.
    Protein Eng Des Sel Volume: 25 Page(s): 7 - 14
    01/01/2012 Authors: McClure M; DeLucas LJ; Wilson L; Ray M; Rowe SM; Wu X; Dai Q; Hong JS; Sorscher EJ; Kappes JC
  • Thermally unstable gating of the most common cystic fibrosis mutant channel (F508): "rescue" by suppressor mutations in nucleotide binding domain 1 and by constitutive mutations in the cytosolic loops.
    J Biol Chem Volume: 286 Page(s): 41937 - 41948
    12/09/2011 Authors: Wang W; Okeyo GO; Tao B; Hong JS; Kirk KL
  • Effect of expression of adenine phosphoribosyltransferase on the in vivo anti-tumor activity of prodrugs activated by E. coli purine nucleoside phosphorylase.
    Cancer Gene Ther Volume: 18 Page(s): 390 - 398
    06/01/2011 Authors: Parker WB; Allan PW; Waud WR; Hong JS; Sorscher EJ
  • A CONSERVED BIOGENESIS NETWORK FOR YEAST YOR1-Delta F AND CFTR-Delta F
    PEDIATRIC PULMONOLOGY Page(s): 277 - 277
    01/01/2011 Authors: Guo J; Louie R; Rodgers JW; White R; Hong J; Sorscher EJ; Bryan JA; Miller EA; Hartman JL
  • IDENTIFICATION OF CFTR POST-TRANSLATIONAL MODIFICATION BY MASS SPECTROMETRY
    PEDIATRIC PULMONOLOGY Page(s): 233 - 233
    01/01/2011 Authors: McClure M; Wilson L; DeLucas LJ; Ray M; Rowe SM; Wu X; Dai Q; Hong J; Kappes JC; Sorscher EJ
  • S-PALMITOYLATION IS A REGULATOR OF CFTR PROCESSING
    PEDIATRIC PULMONOLOGY Page(s): 233 - 233
    01/01/2011 Authors: McClure M; Wilson L; DeLucas LJ; Ray M; Rowe SM; Wu X; Dai Q; Hong JS; Kappes JC; Barnes S
  • A PRO-BIOGENESIS COMPLEX FOR F508DEL-CFTR DISCOVERED WITH A YEAST MODEL AND VALIDATED IN HUMAN CELLS
    PEDIATRIC PULMONOLOGY Page(s): 274 - 274
    01/01/2011 Authors: Hong J; Guo J; Louie R; Wen H; Sorscher EJ; Miller E; Hartman JL
  • Enhanced efficiency of prodrug activation therapy by tumor-selective replicating retrovirus vectors armed with the Escherichia coli purine nucleoside phosphorylase gene.
    Cancer Gene Ther Volume: 17 Page(s): 614 - 623
    09/01/2010 Authors: Tai C-K; Wang W; Lai Y-H; Logg CR; Parker WB; Li Y-F; Hong JS; Sorscher EJ; Chen TC; Kasahara N
  • SCREENING OF CANDIDATE ADENOVIRUS VECTORS EXPRESSING SHRNAS FOR FUNCTIONAL RECOVERY OF Delta F508 CFTR
    PEDIATRIC PULMONOLOGY Page(s): 222 - 223
    01/01/2010 Authors: Sorscher EJ; Hong JS; Hutt DM; Chalfant M; Roth DM; Balch W; Noel S; Frizzell R; Okiyoneda T; Veit G
  • POST-TRANSLATIONAL MODIFICATIONS OF CFTR WITH RELEVANCE TO GATING AND PROCESSING
    PEDIATRIC PULMONOLOGY Page(s): 241 - 241
    01/01/2010 Authors: McClure M; DeLucas LJ; Wilson L; Ray M; Hong JS; Kappes JC; Sorscher EJ; Barnes S
  • RSV INFECTION STIMULATES MMP-9 EXPRESSION & RELEASE FROM HUMAN AIRWAY MONOLAYERS, & REPLICATION IS ABROGATED BY MMP-9 INHIBITION
    PEDIATRIC PULMONOLOGY Page(s): 349 - 349
    01/01/2010 Authors: Maeng P; Li Y; Hong JS; Gaggar A; Clancy JP; Kong M
  • A truncated CFTR protein rescues endogenous DeltaF508-CFTR and corrects chloride transport in mice.
    FASEB J Volume: 23 Page(s): 3743 - 3751
    11/01/2009 Authors: Cormet-Boyaka E; Hong JS; Berdiev BK; Fortenberry JA; Rennolds J; Clancy JP; Benos DJ; Boyaka PN; Sorscher EJ
  • Correlation of microRNA levels during hypoxia with predicted target mRNAs through genome-wide microarray analysis.
    BMC Med Genomics Volume: 2 Page(s): 15
    03/25/2009 Authors: Guimbellot JS; Erickson SW; Mehta T; Wen H; Page GP; Sorscher EJ; Hong JS
  • ANALYSIS OF SYNONYMOUS CFTR POLYMORPHISMS AS CONTRIBUTORS TO CBAVD
    PEDIATRIC PULMONOLOGY Page(s): 276 - 276
    01/01/2009 Authors: Plyler ZE; Bernard KF; Havasi V; Keiles SB; Hong JS; Wen H; Sorscher EJ
  • FLUORESCENCE MICROSCOPY ASSESSMENT OF CFTR MOLECULAR ASSEMBLY
    JOURNAL OF PHYSIOLOGICAL SCIENCES Volume: 59 Page(s): 391 - 391
    01/01/2009 Authors: Berdiev BK; Qadri YJ; Tousson A; Oosterveld-Hut HMJ; Hong JS; Fuller CM; Lukacs GL; Benos DJ
  • Role of oxygen availability in CFTR expression and function.
    Am J Respir Cell Mol Biol Volume: 39 Page(s): 514 - 521
    11/01/2008 Authors: Guimbellot JS; Fortenberry JA; Siegal GP; Moore B; Wen H; Venglarik C; Chen Y-F; Oparil S; Sorscher EJ; Hong JS
  • FRET assessment of CFTR molecular assembly
    FASEB JOURNAL Volume: 22
    04/01/2008 Authors: Berdiev BK; Tousson A; Oosterveld-Hut HMJ; Qadri YJ; Cormet-Boyaka E; Hong JS; Fuller CM; Sorscher EJ; Lukacs GL; Benos DJ
  • Molecular proximity of cystic fibrosis transmembrane conductance regulator and epithelial sodium channel assessed by fluorescence resonance energy transfer.
    J Biol Chem Volume: 282 Page(s): 36481 - 36488
    12/14/2007 Authors: Berdiev BK; Cormet-Boyaka E; Tousson A; Qadri YJ; Oosterveld-Hut HMJ; Hong JS; Gonzales PA; Fuller CM; Sorscher EJ; Lukacs GL
  • Designed zinc finger nucleases to generate cells carrying the Delta 508 genotype at the endogenous CFTR locus
    PEDIATRIC PULMONOLOGY Page(s): 283 - 283
    01/01/2007 Authors: Sun HC; Miller JC; Moehle EA; Rock JM; Holmes MC; Rebar EJ; Hong JS; Sorscher EJ; Urnov F
  • CFTR molecular assembly monitored by FRET
    PEDIATRIC PULMONOLOGY Page(s): 227 - 227
    01/01/2007 Authors: Berdiev BK; Tousson A; Oosterveld-Hut HM; Hong JS; Qadri YJ; Pyle LC; Fuller CM; Lukacs GL; Sorscher EJ; Benos DJ
  • Analysis of microrna expression and CFTR repression during hypoxia
    PEDIATRIC PULMONOLOGY Page(s): 224 - 224
    01/01/2007 Authors: Guimbellot JS; Wen H; Erickson SW; Page GP; Sorscher EJ; Hong JS
  • Characterization of the adenovirus fiber protein.
    Methods Mol Med Volume: 131 Page(s): 281 - 298
    01/01/2007 Authors: Engler JA; Hong JS
  • Activators of viral gene expression in polarized epithelial monolayers identified by rapid-throughput drug screening.
    Gene Ther Volume: 13 Page(s): 781 - 788
    05/01/2006 Authors: Sorscher EJ; Harris J; Alexander M; Rottgers A; Hardy K; Ponnazhagan S; Collawn JF; McClintock J; Amsler CD; Webster A
  • Micro-RNA-like effects of complete intronic sequences.
    Front Biosci Volume: 11 Page(s): 1998 - 2006
    05/01/2006 Authors: Hill AE; Hong JS; Wen H; Teng L; McPherson DT; McPherson SA; Levasseur DN; Sorscher EJ
  • Antibiotic-mediated chemoprotection enhances adaptation of E. coli PNP for herpes simplex virus-based glioma therapy.
    Hum Gene Ther Volume: 16 Page(s): 339 - 347
    03/01/2005 Authors: Bharara S; Sorscher EJ; Gillespie GY; Lindsey JR; Hong JS; Curlee KV; Allan PW; Gadi VK; Alexander SA; Secrist JA
  • Excellent in vivo bystander activity of fludarabine phosphate against human glioma xenografts that express the escherichia coli purine nucleoside phosphorylase gene.
    Cancer Res Volume: 64 Page(s): 6610 - 6615
    09/15/2004 Authors: Hong JS; Waud WR; Levasseur DN; Townes TM; Wen H; McPherson SA; Moore BA; Bebok Z; Allan PW; Secrist JA
  • Hepatocyte growth factor stimulates adenoviral-mediated gene transfer across the apical membrane of epithelial cells.
    J Gene Med Volume: 6 Page(s): 624 - 630
    06/01/2004 Authors: Burrus JK; Matheson WD; Hong JS; Sorscher EJ; Balkovetz DF
  • Efficient intracellular processing of the endogenous cystic fibrosis transmembrane conductance regulator in epithelial cell lines.
    J Biol Chem Volume: 279 Page(s): 22578 - 22584
    05/21/2004 Authors: Varga K; Jurkuvenaite A; Wakefield J; Hong JS; Guimbellot JS; Venglarik CJ; Niraj A; Mazur M; Sorscher EJ; Collawn JF
  • Designer gene therapy using an Escherichia coli purine nucleoside phosphorylase/prodrug system.
    Chem Biol Volume: 10 Page(s): 1173 - 1181
    12/01/2003 Authors: Bennett EM; Anand R; Allan PW; Hassan AEA; Hong JS; Levasseur DN; McPherson DT; Parker WB; Secrist JA; Sorscher EJ
  • Membrane transplantation to correct integral membrane protein defects.
    J Mol Med (Berl) Volume: 81 Page(s): 511 - 520
    08/01/2003 Authors: Curlee KV; Hong JS; Clancy JP; King SA; Hunter E; Berdiev B; Benos D; Sommerfelt MA; Sorscher EJ; Sakalian M
  • Evidence that systemic gentamicin suppresses premature stop mutations in patients with cystic fibrosis.
    Am J Respir Crit Care Med Volume: 163 Page(s): 1683 - 1692
    06/01/2001 Authors: Clancy JP; Bebk Z; Ruiz F; King C; Jones J; Walker L; Greer H; Hong J; Wing L; Macaluso M
  • A clinical inflammatory syndrome attributable to aerosolized lipid-DNA administration in cystic fibrosis.
    Hum Gene Ther Volume: 12 Page(s): 751 - 761
    05/01/2001 Authors: Ruiz FE; Clancy JP; Perricone MA; Bebok Z; Hong JS; Cheng SH; Meeker DP; Young KR; Schoumacher RA; Weatherly MR
  • Effective gene transfer into regenerating sciatic nerves by adenoviral vectors: potentials for gene therapy of peripheral nerve injury.
    Mol Cells Volume: 10 Page(s): 540 - 545
    10/31/2000 Authors: Joung I; Kim HS; Hong JS; Kwon H; Kwon YK
  • CFTR processing and degradation at the endoplasmic reticulum
    FASEB JOURNAL Volume: 13 Page(s): A730 - A730
    03/15/1999 Authors: Bebok Z; Hicks JK; King S; Hong JS; Sorscher EJ
  • The mechanism underlying cystic fibrosis transmembrane conductance regulator transport from the endoplasmic reticulum to the proteasome includes Sec61beta and a cytosolic, deglycosylated intermediary.
    J Biol Chem Volume: 273 Page(s): 29873 - 29878
    11/06/1998 Authors: Bebk Z; Mazzochi C; King SA; Hong JS; Sorscher EJ
  • Cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide-binding domain 1 (NBD-1) and CFTR truncated within NBD-1 target to the epithelial plasma membrane and increase anion permeability.
    Biochemistry Volume: 37 Page(s): 15222 - 15230
    10/27/1998 Authors: Clancy JP; Hong JS; Bebk Z; King SA; Demolombe S; Bedwell DM; Sorscher EJ
  • Suppression of a CFTR premature stop mutation in a bronchial epithelial cell line.
    Nat Med Volume: 3 Page(s): 1280 - 1284
    11/01/1997 Authors: Bedwell DM; Kaenjak A; Benos DJ; Bebok Z; Bubien JK; Hong J; Tousson A; Clancy JP; Sorscher EJ
  • Modulation of adenovirus-mediated gene transfer by nitric oxide.
    Am J Respir Cell Mol Biol Volume: 16 Page(s): 501 - 509
    05/01/1997 Authors: Haddad IY; Sorscher EJ; Garver RI; Hong J; Tzeng E; Matalon S
  • Isolation of a common receptor for Coxsackie B viruses and adenoviruses 2 and 5.
    Science Volume: 275 Page(s): 1320 - 1323
    02/28/1997 Authors: Bergelson JM; Cunningham JA; Droguett G; Kurt-Jones EA; Krithivas A; Hong JS; Horwitz MS; Crowell RL; Finberg RW
  • Transiently overexpressed phosphoglucomutase colocalizes with the endoplasmic reticulum and the cytosol
    MOLECULAR BIOLOGY OF THE CELL Volume: 7 Page(s): 766 - 766
    12/01/1996 Authors: Bounelis P; Hong JS; Martone MA; Veyna N; Ellisman MH; Marchase RB
  • Domains required for assembly of adenovirus type 2 fiber trimers.
    J Virol Volume: 70 Page(s): 7071 - 7078
    10/01/1996 Authors: Hong JS; Engler JA
  • Addition of a short peptide ligand to the adenovirus fiber protein.
    Gene Ther Volume: 2 Page(s): 660 - 668
    11/01/1995 Authors: Michael SI; Hong JS; Curiel DT; Engler JA
  • MAMMALIAN PHOSPHOGLUCOMUTASE IS AN AMBIQUITOUS GLYCOPROTEIN
    FASEB JOURNAL Volume: 9 Page(s): A411 - A411
    03/09/1995 Authors: BOUNELIS P; MARTONE MA; ELLISMAN MH; HONG JS; ENGLER JA; MARCHASE RB
  • ASSEMBLY OF FIBER TRIMERS FROM HUMAN ADENOVIRUS TYPE-2
    FASEB JOURNAL Volume: 7 Page(s): A1302 - A1302
    04/20/1993 Authors: MULACH BL; HONG JS; ENGLER JA
  • The amino terminus of the adenovirus fiber protein encodes the nuclear localization signal.
    Virology Volume: 185 Page(s): 758 - 767
    12/01/1991 Authors: Hong JS; Engler JA
  • REQUIREMENTS FOR CORRECT NUCLEAR TARGETING OF ADENOVIRUS FIBER
    FASEB JOURNAL Volume: 5 Page(s): A1556 - A1556
    03/19/1991 Authors: HONG JS; ENGLER JA
  • Characterization of the early region 3 and fiber genes of Ad7.
    Virology Volume: 167 Page(s): 545 - 553
    12/01/1988 Authors: Hong JS; Mullis KG; Engler JA
  • Nucleotide sequence of the genes encoded in early region 2b of human adenovirus type 12.
    Gene Volume: 46 Page(s): 187 - 195
    01/01/1986 Authors: Shu LM; Hong JS; Wei YF; Engler JA
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