Publications

• Flow cytometric measurement of CFTR-mediated chloride transport in human neutrophils.
  J Leukoc Biol Volume: 117
  04/23/2025 Authors: Montanez-Barragan A; Robledo-Avila FH; Rascon R; McCoy KS; Kopp BT; Partida-Sanchez S
• Effects of Therapeutic Antibiotic Exposure on the Oropharyngeal and Fecal Microbiota in Infants With Cystic Fibrosis.
  Pediatr Pulmonol Volume: 60 Page(s): e71024
  03/01/2025 Authors: Hayden HS; Nelson MT; Ross SE; Verster AJ; Bouzek DC; Eng A; Waalkes A; Penewit K; Kopp BT; Siracusa C
• Secondhand vape exposure regulation of CFTR and immune function in cystic fibrosis.
  Am J Physiol Lung Cell Mol Physiol Volume: 328 Page(s): L324 - L333
  03/01/2025 Authors: Wisniewski BL; Shrestha M; Bojja D; Shrestha CL; Lee CS; Ozuna H; Rayner RE; Bai S; Cormet-Boyaka E; Reynolds SD
• Proteomics profiling of inflammatory responses to elexacaftor/tezacaftor/ivacaftor in cystic fibrosis.
  Front Immunol Volume: 16 Page(s): 1486784
  01/01/2025 Authors: Ozuna H; Bojja D; Partida-Sanchez S; Hall-Stoodley L; Amer A; Britt RD; Sheikh S; Frank DA; Wang W; Kang B-Y
• ENaC contributes to macrophage dysfunction in cystic fibrosis.
  bioRxiv
  11/08/2024 Authors: Moran J; Pugh C; Brown N; Thomas A; Zhang S; McCauley E; Cephas A; Shrestha CL; Partida-Sanchez S; Bai S
• PPAR/ETV2 axis regulates endothelial-to-mesenchymal transition in pulmonary hypertension.
  Pulm Circ Volume: 14 Page(s): e12448
  10/01/2024 Authors: Lee DH; Kim M; Chang SS; Lee R; Jang AJ; Kim J; Ma J; Passineau MJ; Benza RL; Karmouty-Quintana H
• Updates in Pediatric Sickle Cell Lung Disease.
  Clin Chest Med Volume: 45 Page(s): 749 - 760
  09/01/2024 Authors: Gillespie M; Afolabi-Brown O; Machogu E; Willen S; Kopp BT
• Pseudomonas aeruginosa Lipid A Structural Variants Induce Altered Immune Responses.
  Am J Respir Cell Mol Biol Volume: 71 Page(s): 207 - 218
  08/01/2024 Authors: Hofstaedter CE; O'Keefe IP; Met CM; Wu L; Vanderwoude J; Shin S; Diggle SP; Riquelme SA; Rasko DA; Doi Y
• Innate immune responses are increased in children with acute asthma exacerbation.
  Pediatr Allergy Immunol Volume: 35 Page(s): e14173
  06/01/2024 Authors: Sheikh S; Eisner M; Walum J; Heyob K; Khan AQ; Lewis B; Grayson M; Kopp B; McCoy K; Britt R
• Nasal airway inflammatory responses and pathogen detection in infants with cystic fibrosis.
  J Cyst Fibros Volume: 23 Page(s): 219 - 225
  03/01/2024 Authors: Kopp BT; Ross SE; Bojja D; Guglani L; Chandler JD; Tirouvanziam R; Thompson M; Slaven JE; Chmiel JF; Siracusa C
• Purposeful Podiums: Ensuring Speaker Diversity at the American Thoracic Society International Conference.
  Ann Am Thorac Soc Volume: 20 Page(s): 1361 - 1363
  09/01/2023 Authors: Laguna TA; Kopp BT; Brown-Janowiak D; Guerrero N; Rose L; Wagner B; Moore PE
• Description of a Colocated Comprehensive Care Model for People With Sickle Cell and Comorbid Pulmonary Disease.
  J Pediatr Hematol Oncol Volume: 45 Page(s): e723 - e727
  08/01/2023 Authors: Pugh C; Zeno RN; Stanek J; Gillespie M; Kopp BT; Creary SE
• Outcomes before and after providing interdisciplinary hematology and pulmonary care for children with sickle cell disease.
  Blood Adv Volume: 7 Page(s): 2245 - 2251
  05/23/2023 Authors: Zeno RN; Stanek J; Pugh C; Gillespie M; Kopp BT; Creary S
• Cystic fibrosis macrophage function and clinical outcomes after elexacaftor/tezacaftor/ivacaftor.
  Volume: 61
  04/01/2023 Authors: Zhang S; Shrestha CL; Robledo-Avila F; Jaganathan D; Wisniewski BL; Brown N; Pham H; Carey K; Amer AO; Hall-Stoodley L
• Impact of elexacaftor-tezacaftor-ivacaftor on bacterial colonization and inflammatory responses in cystic fibrosis.
  Pediatr Pulmonol Volume: 58 Page(s): 825 - 833
  03/01/2023 Authors: Sheikh S; Britt RD; Ryan-Wenger NA; Khan AQ; Lewis BW; Gushue C; Ozuna H; Jaganathan D; McCoy K; Kopp BT
• Cryptogenic organizing pneumonia: In the setting of Staphylococcus aureus endocarditis.
  Pediatr Pulmonol Volume: 58 Page(s): 325 - 327
  01/01/2023 Authors: Mull ES; Cohen S; George A; Krivchenia K; Druhan S; Baker PB; Kopp B
• Long-term pulmonary sequelae in adolescents post-SARS-CoV-2 infection.
  Pediatr Pulmonol Volume: 57 Page(s): 2455 - 2463
  10/01/2022 Authors: Palacios S; Krivchenia K; Eisner M; Young B; Ramilo O; Mejias A; Lee S; Kopp BT
• Emerging Concepts in Defective Macrophage Phagocytosis in Cystic Fibrosis.
  Int J Mol Sci Volume: 23
  07/13/2022 Authors: Jaganathan D; Bruscia EM; Kopp BT
• Hypervitaminosis A with fulminant secondary intracranial hypertension following personalized medicine-based Elexacaftor/Tezacaftor/Ivacaftor initiation in a preadolescent with cystic fibrosis.
  J Cyst Fibros Volume: 21 Page(s): e217 - e220
  05/01/2022 Authors: Wisniewski BL; Aylward SC; Jordan CO; Kopp BT; Paul GR
• Staphylococcus Aureus Endocarditis Complicated by Cryptogenic Organizing Pneumonia
  Volume: 205
  05/01/2022 Authors: Mull ES; Kopp BT
• Sweat metabolomics before and after intravenous antibiotics for pulmonary exacerbation in people with cystic fibrosis.
  Respir Med Volume: 191 Page(s): 106687
  01/01/2022 Authors: Woodley FW; Gecili E; Szczesniak RD; Shrestha CL; Nemastil CJ; Kopp BT; Hayes D
• Advocacy Considerations for the Pediatric Pulmonologist in the Era of the COVID-19 Pandemic.
  Ann Am Thorac Soc Volume: 18 Page(s): 942 - 945
  06/01/2021 Authors: Rao DR; Kopp B; Kamerman-Kretzmer RJ; Afolabi F; Liptzin DR; Balasubramaniam V; Sadreameli SC
• Functional CFTR channel is essential for effective antimicrobial activities of neutrophils
  Volume: 206
  05/01/2021 Authors: Hanz F; Avila R; Kopp BT; Partida-Sanchez S
• Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1.
  Autophagy Volume: 17 Page(s): 1 - 382
  01/01/2021 Authors: Klionsky DJ; Abdel-Aziz AK; Abdelfatah S; Abdellatif M; Abdoli A; Abel S; Abeliovich H; Abildgaard MH; Abudu YP; Acevedo-Arozena A
• (R)-Roscovitine and CFTR modulators enhance killing of multi-drug resistant Burkholderia cenocepacia by cystic fibrosis macrophages.
  Sci Rep Volume: 10 Page(s): 21700
  12/10/2020 Authors: Shrestha CL; Zhang S; Wisniewski B; Hfner S; Elie J; Meijer L; Kopp BT
• EFFECTS OF CFTR MODULATORS ON CFTR EXPRESSION AND THE ANTIMICROBIAL FUNCTIONS OF CF NEUTROPHILS
  Volume: 55 Page(s): S141 - S141
  10/01/2020 Authors: Avila RFH; Shrestha C; Kopp BT; Partida-Sanchez S
• Upper airway microbiome changes in children with sickle cell disease during vaso-occlusive and acute chest syndrome episodes.
  Am J Hematol Volume: 95 Page(s): E289 - E292
  10/01/2020 Authors: Loman BR; Shrestha CL; Kotha K; Minta A; Zhang S; Mejias A; Bailey MT; Creary S; Kopp BT
• Metabolomics profiling of tobacco exposure in children with cystic fibrosis.
  J Cyst Fibros Volume: 19 Page(s): 791 - 800
  09/01/2020 Authors: Wisniewski BL; Shrestha CL; Zhang S; Thompson R; Gross M; Groner JA; Uppal K; Ramilo O; Mejias A; Kopp BT
• Author Correction: Baseline and Disease-Induced Transcriptional Profiles in Children with Sickle Cell Disease.
  Sci Rep Volume: 10 Page(s): 13530
  08/06/2020 Authors: Creary S; Shrestha CL; Kotha K; Minta A; Fitch J; Jaramillo L; Zhang S; Pinto S; Thompson R; Ramilo O
• Age and environmental exposures influence the fecal bacteriome of young children with cystic fibrosis.
  Pediatr Pulmonol Volume: 55 Page(s): 1661 - 1670
  07/01/2020 Authors: Loman BR; Shrestha CL; Thompson R; Groner JA; Mejias A; Ruoff KL; O'Toole GA; Bailey MT; Kopp BT
• Baseline and Disease-Induced Transcriptional Profiles in Children with Sickle Cell Disease.
  Sci Rep Volume: 10 Page(s): 9013
  06/02/2020 Authors: Creary S; Shrestha CL; Kotha K; Minta A; Fitch J; Jaramillo L; Zhang S; Pinto S; Thompson R; Ramilo O
• Whole-blood transcriptomic responses to lumacaftor/ivacaftor therapy in cystic fibrosis.
  J Cyst Fibros Volume: 19 Page(s): 245 - 254
  03/01/2020 Authors: Kopp BT; Fitch J; Jaramillo L; Shrestha CL; Robledo-Avila F; Zhang S; Palacios S; Woodley F; Hayes D; Partida-Sanchez S
• Oral cysteamine as an adjunct treatment in cystic fibrosis pulmonary exacerbations: An exploratory randomized clinical trial.
  PLoS One Volume: 15 Page(s): e0242945
  01/01/2020 Authors: Devereux G; Wrolstad D; Bourke SJ; Daines CL; Doe S; Dougherty R; Franco R; Innes A; Kopp BT; Lascano J
• Consequences of CRISPR-Cas9-Mediated CFTR Knockout in Human Macrophages.
  Front Immunol Volume: 11 Page(s): 1871
  01/01/2020 Authors: Zhang S; Shrestha CL; Wisniewski BL; Pham H; Hou X; Li W; Dong Y; Kopp BT
• Multi-Omics Profiling of Sickle Cell Acute Chest Syndrome
  Volume: 201
  01/01/2020 Authors: Kopp BT; Creary S; Loman B; Shrestha C; Kotha K; Minta A; Zhang S; Pinto SJ; Thompson RA; Ramilo O
• Secondhand Smoke Exposure and Serum Trypsinogen in Cystic Fibrosis Carriers.
  Pancreas Volume: 48 Page(s): 1155 - 1159
  10/01/2019 Authors: Ellery KM; Kopp B; Conwell DL; Gariepy C
• IMPACT OF CFTR-RELATED IMMUNE DYSFUNCTION ON INFECTION
  Volume: 54 Page(s): S139 - S139
  10/01/2019 Authors: Kopp BT
• PROLONGED NEUTRALIZATION OF ACID GASTROESOPHAGEAL REFLUX DURING CHEMICAL CLEARANCE IN CHILDREN WITH CYSTIC FIBROSIS IS NOT LIKELY DUE TO REDUCED EFFICIENCY IN SALIVA TRANSPORT
  Volume: 54 Page(s): S257 - S258
  10/01/2019 Authors: Woodley FW; Ciciora SL; Hayes D; Kopp BT; Williams K; Nemastil C; Di Lorenzo C; Kaul A; Mousa H
• DEVELOPING CFTR-KNOCKOUT HUMAN MONOCYTE-DERIVED MACROPHAGES
  Volume: 54 Page(s): S180 - S180
  10/01/2019 Authors: Zhang S; Shrestha C; Dong Y; Hou X; Kopp BT
• ROSCOVITINE (SELICICLIB) ENHANCES KILLING OF MULTIDRUG RESISTANT BURKHOLDERIA CENOCEPACIA BY CF MONOCYTE-DERIVED MACROPHAGES
  Volume: 54 Page(s): S181 - S181
  10/01/2019 Authors: Shrestha C; Zhang S; Elie J; Meijer L; Kopp BT
• Identifying Clinical and Research Priorities in Sickle Cell Lung Disease. An Official American Thoracic Society Workshop Report.
  Ann Am Thorac Soc Volume: 16 Page(s): e17 - e32
  03/01/2009 Authors: Ruhl AP; Sadreameli SC; Allen JL; Bennett DP; Campbell AD; Coates TD; Diallo DA; Field JJ; Fiorino EK; Gladwin MT
• AR-13 reduces antibiotic-resistant bacterial burden in cystic fibrosis phagocytes and improves cystic fibrosis transmembrane conductance regulator function.
  J Cyst Fibros Volume: 18 Page(s): 622 - 629
  09/01/2019 Authors: Assani K; Shrestha CL; Rinehardt H; Zhang S; Robledo-Avila F; Wellmerling J; Partida-Sanchez S; Cormet-Boyaka E; Reynolds SD; Schlesinger LS
• Urinary metabolomics reveals unique metabolic signatures in infants with cystic fibrosis.
  J Cyst Fibros Volume: 18 Page(s): 507 - 515
  07/01/2019 Authors: Kopp BT; Joseloff E; Goetz D; Ingram B; Heltshe SL; Leung DH; Ramsey BW; McCoy K; Borowitz D
• Pulmonary findings in infants with cystic fibrosis during the first year of life: Results from the Baby Observational and Nutrition Study (BONUS) cohort study.
  Pediatr Pulmonol Volume: 54 Page(s): 581 - 586
  05/01/2019 Authors: Goetz D; Kopp BT; Salvator A; Moore-Clingenpeel M; McCoy K; Leung DH; Kloster M; Ramsey BR; Heltshe SH; Borowitz D
• Secondhand smoke alters arachidonic acid metabolism and inflammation in infants and children with cystic fibrosis.
  Thorax Volume: 74 Page(s): 237 - 246
  03/01/2019 Authors: Kopp BT; Thompson R; Kim J; Konstan R; Diaz A; Smith B; Shrestha C; Rogers LK; Hayes D; Tumin D
• Cell Therapy for Cystic Fibrosis Lung Disease: Regenerative Basal Cell Amplification.
  Stem Cells Transl Med Volume: 8 Page(s): 225 - 235
  03/01/2019 Authors: Hayes D; Kopp BT; Hill CL; Lallier SW; Schwartz CM; Tadesse M; Alsudayri A; Reynolds SD
• Correction: IFN- Stimulates Autophagy-Mediated Clearance of Burkholderia cenocepacia in Human Cystic Fibrosis Macrophages.
  PLoS One Volume: 14 Page(s): e0213092
  01/01/2019 Authors: Assani K; Tazi MF; Amer AO; Kopp BT
• Gastroesophageal reflux in cystic fibrosis across the age spectrum.
  Transl Gastroenterol Hepatol Volume: 4 Page(s): 69
  01/01/2019 Authors: Woodley FW; Hayes D; Kopp BT; Moore-Clingenpeel M; Machado RS; Nemastil CJ; Jadcherla S; Di Lorenzo C; Kaul A; Mousa H
• Influence of CFTR Modulators on Immune Responses in Cystic Fibrosis
  Volume: 199
  01/01/2019 Authors: Kopp BT; Zhang S; Shrestha C
• Cystic fibrosis transmembrane conductance regulator (CFTR) modulators have differential effects on cystic fibrosis macrophage function.
  Sci Rep Volume: 8 Page(s): 17066
  11/20/2018 Authors: Zhang S; Shrestha CL; Kopp BT
• Dysregulated Calcium Homeostasis in Cystic Fibrosis Neutrophils Leads to Deficient Antimicrobial Responses.
  J Immunol Volume: 201 Page(s): 2016 - 2027
  10/01/2018 Authors: Robledo-Avila FH; Ruiz-Rosado JDD; Brockman KL; Kopp BT; Amer AO; McCoy K; Bakaletz LO; Partida-Sanchez S
• CARE-CF-1 TRIAL: CYSTEAMINE, AN ORAL ADJUNCT TO STANDARD OF CARE INTERVENTIONS IN CF INFECTIOUS EXACERBATIONS
  Volume: 53 Page(s): 260 - 260
  09/01/2018 Authors: Devereux G; Bourke S; Daines C; Doe S; Dougherty R; Franco R; Innes A; Kopp BT; Lascano J; Laysih D
• DO CFTR MODULATORS AFFECT MACROPHAGE AUTOPHAGY AND ER STRESS?
  Volume: 53 Page(s): 280 - 280
  09/01/2018 Authors: Zhang S; Shrestha C; Bah A; Kopp BT
• CHILDREN WITH CYSTIC FIBROSIS AND GERD HAVE SIGNIFICANTLY LOWER PROXIMAL BASELINE IMPEDANCE WHEN COMPARED TO SYMPTOMATIC CHILDREN WITHOUT CYSTIC FIBROSIS
  Volume: 53 Page(s): 384 - 385
  09/01/2018 Authors: Woodley FW; Moore-Clingenpeel M; Nemastil CJ; Machado RS; Hayes D; Kopp BT; Kaul A; Di Lorenzo C; Mousa H; Jadcherla S
• Benefits of pulmonary rehabilitation in pediatric asthma.
  Volume: 53 Page(s): 1014 - 1017
  08/01/2018 Authors: Kirkby S; Rossetti A; Hayes D; Allen E; Sheikh S; Kopp B; Patel A
• The expression of Mirc1/Mir17-92 cluster in sputum samples correlates with pulmonary exacerbations in cystic fibrosis patients.
  J Cyst Fibros Volume: 17 Page(s): 454 - 461
  07/01/2018 Authors: Krause K; Kopp BT; Tazi MF; Caution K; Hamilton K; Badr A; Shrestha C; Tumin D; Hayes D; Robledo-Avila F
• A Quality Improvement Approach to Increasing Smoking Cessation Counseling in Cystic Fibrosis Patients
  Volume: 142
  05/01/2018 Authors: Bauer SE; Kramer JL; Khalfoun S; Kopp BT; Groner JA; Goleman J
• Metabolomic responses to lumacaftor/ivacaftor in cystic fibrosis.
  Pediatr Pulmonol Volume: 53 Page(s): 583 - 591
  05/01/2018 Authors: Kopp BT; McCulloch S; Shrestha CL; Zhang S; Sarzynski L; Woodley FW; Hayes D
• Multi-Omics Profiling of Lumacaftor/Ivacaftor Response in Cystic Fibrosis
  Volume: 197
  01/01/2018 Authors: Kopp BT; Fitch JR; Zhang S; Shrestha CL; Woodley FW; Hayes D; White P
• Impact of Presence of Children on Indoor Tobacco Restrictions in Households of Urban and Rural Adult Tobacco Users.
  Acad Pediatr Volume: 18 Page(s): 920 - 927
  01/01/2018 Authors: Kopp BT; Hinton A; Lu R; Cooper S; Nagaraja H; Wewers ME
• EXHALED BREATH CONDENSATE IS NOT LIKELY A VIABLE SUBSTITUTE FOR BRONCHOALVEOLAR LAVAGE
  Volume: 52 Page(s): S259 - S259
  09/01/2017 Authors: Woodley FW; Hayes JD; Kopp BT; Nemastil CJ; He Z; Di Lorenzo C; Jadcherla S
• CFTR MODULATOR IMPACT ON MACROPHAGE FUNCTION
  Volume: 52 Page(s): S244 - S244
  09/01/2017 Authors: Shrestha C; Zhang S; Konstan R; Kopp BT
• Not All Children with Cystic Fibrosis Have Abnormal Esophageal Neutralization during Chemical Clearance of Acid Reflux.
  Pediatr Gastroenterol Hepatol Nutr Volume: 20 Page(s): 153 - 159
  09/01/2017 Authors: Woodley FW; Moore-Clingenpeel M; Machado RS; Nemastil CJ; Jadcherla SR; Hayes D; Kopp BT; Kaul A; Di Lorenzo C; Mousa H
• Transplant center volume and outcomes in lung transplantation for cystic fibrosis.
  Transpl Int Volume: 30 Page(s): 371 - 377
  04/01/2017 Authors: Hayes D; Sweet SC; Benden C; Kopp BT; Goldfarb SB; Visner GA; Mallory GB; Tobias JD; Tumin D
• The effect of the affordable care act dependent coverage provision on patients with cystic fibrosis.
  Pediatr Pulmonol Volume: 52 Page(s): 458 - 466
  04/01/2017 Authors: Tumin D; Li SS; Kopp BT; Kirkby SE; Tobias JD; Morgan WJ; Hayes D
• Human Cystic Fibrosis Macrophages Have Defective Calcium-Dependent Protein Kinase C Activation of the NADPH Oxidase, an Effect Augmented by Burkholderia cenocepacia.
  J Immunol Volume: 198 Page(s): 1985 - 1994
  03/01/2017 Authors: Assani K; Shrestha CL; Robledo-Avila F; Rajaram MV; Partida-Sanchez S; Schlesinger LS; Kopp BT
• Cysteamine-mediated clearance of antibiotic-resistant pathogens in human cystic fibrosis macrophages.
  PLoS One Volume: 12 Page(s): e0186169
  01/01/2017 Authors: Shrestha CL; Assani KD; Rinehardt H; Albastroiu F; Zhang S; Shell R; Amer AO; Schlesinger LS; Kopp BT
• Pretransplant Panel Reactive Antibodies and Lung Transplant Outcomes in Children.
  Thorac Cardiovasc Surg Volume: 65 Page(s): 36 - 42
  01/01/2017 Authors: Hayes D; Kopp BT; Sheikh SI; Shell RD; Paul GR; McConnell PI; Tobias JD; Tumin D
• Cysteamine-Mediated Clearance Of Multi-Drug Resistant Pathogens From Cystic Fibrosis Macrophages
  Volume: 195
  01/01/2017 Authors: Kopp BT; Shrestha C; Assani K; Schlesinger LS
• Cell Therapy For Cystic Fibrosis: Is There An Optimal Source Of Basal Progenitor Cells?
  Volume: 195
  01/01/2017 Authors: Hayes D; Tumin D; Aggarwall R; Lallier S; Hill C; Kopp BT; Nemastil CJ; Reynolds SD
• Secondhand Smoke Is an Important Modifiable Risk Factor in Sickle Cell Disease: A Review of the Current Literature and Areas for Future Research.
  Int J Environ Res Public Health Volume: 13
  11/12/2016 Authors: Sadreameli SC; Kopp BT; Creary SE; Eakin MN; McGrath-Morrow S; Strouse JJ
• Elevated Mirc1/Mir17-92 cluster expression negatively regulates autophagy and CFTR (cystic fibrosis transmembrane conductance regulator) function in CF macrophages.
  Autophagy Volume: 12 Page(s): 2026 - 2037
  11/01/2016 Authors: Tazi MF; Dakhlallah DA; Caution K; Gerber MM; Chang S-W; Khalil H; Kopp BT; Ahmed AE; Krause K; Davis I
• The Impact of Secondhand Smoke Exposure on Children with Cystic Fibrosis: A Review.
  Int J Environ Res Public Health Volume: 13
  10/12/2016 Authors: Kopp BT; Ortega-Garca JA; Sadreameli SC; Wellmerling J; Cormet-Boyaka E; Thompson R; McGrath-Morrow S; Groner JA
• TRANSCRIPTIONAL PROFILING IN YOUNG CHILDREN WITH CYSTIC FIBROSIS REVEALS NOVEL TARGETS ACCORDING TO AGE
  Volume: 51 Page(s): 266 - 266
  10/01/2016 Authors: Kopp BT; Smith B; Thompson R; Hayes D; Ramilo O; Mejias A
• TRANSPLANT CENTER CYSTIC FIBROSIS-SPECIFIC EXPERTISE AND OUTCOME OF LUNG TRANSPLANTATION
  Volume: 51 Page(s): 378 - 378
  10/01/2016 Authors: Hayes JD; Tumin D; Kirkby SE; Mansour HM; Tobias JD; Kopp BT
• Influence of graft ischemic time on survival in children with cystic fibrosis after lung transplantation.
  Pediatr Pulmonol Volume: 51 Page(s): 908 - 913
  09/01/2016 Authors: Hayes D; Tumin D; Kopp BT; Tobias JD; Sheikh SI; Kirkby SE
• Impact of Donor Arterial Partial Pressure of Oxygen on Outcomes After Lung Transplantation in Adult Cystic Fibrosis Recipients.
  Lung Volume: 194 Page(s): 547 - 553
  08/01/2016 Authors: Hayes D; Kopp BT; Kirkby SE; Reynolds SD; Mansour HM; Tobias JD; Tumin D
• Characteristics of invasive Acinetobacter species isolates recovered in a pediatric academic center.
  BMC Infect Dis Volume: 16 Page(s): 346
  07/22/2016 Authors: Jain AL; Harding CM; Assani K; Shrestha CL; Haga M; Leber A; Munson RS; Kopp BT
• Aging is associated with hypermethylation of autophagy genes in macrophages.
  Epigenetics Volume: 11 Page(s): 381 - 388
  05/03/2016 Authors: Khalil H; Tazi M; Caution K; Ahmed A; Kanneganti A; Assani K; Kopp B; Marsh C; Dakhlallah D; Amer AO
• The Geographic Impact on Hospitalization in Patients with Cystic Fibrosis.
  J Pediatr Volume: 170 Page(s): 246-52.e1-4
  03/01/2016 Authors: Kopp BT; Nicholson L; Paul G; Tobias J; Ramanathan C; Hayes D
• Influence of human leukocyte antigen mismatching on bronchiolitis obliterans syndrome in lung transplantation.
  J Heart Lung Transplant Volume: 35 Page(s): 186 - 194
  02/01/2016 Authors: Hayes D; Black SM; Tobias JD; Kopp BT; Kirkby SE; Mansour HM; Whitson BA
• Pilot trial of light therapy for depression in hospitalized patients with cystic fibrosis.
  J Affect Disord Volume: 189 Page(s): 164 - 168
  01/01/2016 Authors: Kopp BT; Hayes D; Ghera P; Patel A; Kirkby S; Kowatch RA; Splaingard M
• Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition).
  Autophagy Volume: 12 Page(s): 1 - 222
  01/01/2016 Authors: Klionsky DJ; Abdelmohsen K; Abe A; Abedin MJ; Abeliovich H; Acevedo Arozena A; Adachi H; Adams CM; Adams PD; Adeli K
• Erratum.
  Autophagy Volume: 12 Page(s): 443
  01/01/2016
• Donor Arterial Partial Pressure Of Oxygen And Outcomes After Lung Transplantation In Children With Cystic Fibrosis
  Volume: 193
  01/01/2016 Authors: Hayes D; Tumin D; Reynolds SD; Malleske D; Tobias J; Kopp BT
• The Influence Of Secondhand Smoke Exposure On Arachidonic Acid Metabolism And Outcomes In Infants And Young Children With Cystic Fibrosis
  Volume: 193
  01/01/2016 Authors: Kopp BT; Rogers LK; Mejias A; Hayes D; Tumin D; Woodley F; Thompson R; Groner J
• Cigarette Smoking Effect on Survival After Lung Transplant in Cystic Fibrosis.
  Exp Clin Transplant Volume: 13 Page(s): 529 - 534
  12/01/2015 Authors: Kopp BT; Groner J; Tobias JD; Whitson BA; Kirkby S; Hayes D
• Survival in Patients with Advanced Non-cystic Fibrosis Bronchiectasis Versus Cystic Fibrosis on the Waitlist for Lung Transplantation.
  Lung Volume: 193 Page(s): 933 - 938
  12/01/2015 Authors: Hayes D; Kopp BT; Tobias JD; Woodley FW; Mansour HM; Tumin D; Kirkby SE
• IMPACT OF GENDER ON SURVIVAL AMONG PATIENTS WITH CYSTIC FIBROSIS LISTED FOR LUNG TRANSPLANTATION
  Volume: 50 Page(s): 372 - 372
  10/01/2015 Authors: Kirkby SE; Kopp BT; Tobias J; Patel A; McCoy KS
• AR-13 AS A POTENTIAL NEW THERAPEUTIC FOR REDUCING BURKHOLDERIA CENOCEPACIA BURDEN IN CF MACROPHAGES
  Volume: 50 Page(s): 311 - 311
  10/01/2015 Authors: Rinehardt H; Assani K; Shrestha C; Schlesinger LS; Kopp BT
• Eucapnic Voluntary Hyperventilation to Detect Exercise-Induced Bronchoconstriction in Cystic Fibrosis.
  Lung Volume: 193 Page(s): 733 - 738
  10/01/2015 Authors: Kirkby SE; Hayes D; Parsons JP; Wisely CE; Kopp B; McCoy KS; Mastronarde JG
• Mortality Risk and Pulmonary Function in Adults With Cystic Fibrosis at Time of Wait Listing for Lung Transplantation.
  Ann Thorac Surg Volume: 100 Page(s): 474 - 479
  08/01/2015 Authors: Hayes D; Kirkby S; Whitson BA; Black SM; Sheikh SI; Tobias JD; Mansour HM; Kopp BT
• Geographic variations in cystic fibrosis: An analysis of the U.S. CF Foundation Registry.
  Pediatr Pulmonol Volume: 50 Page(s): 754 - 762
  08/01/2015 Authors: Kopp BT; Nicholson L; Paul G; Tobias J; Ramanathan C; Hayes D
• Detrimental effects of secondhand smoke exposure on infants with cystic fibrosis.
  Pediatr Pulmonol Volume: 50 Page(s): 25 - 34
  01/01/2015 Authors: Kopp BT; Sarzynski L; Khalfoun S; Hayes D; Thompson R; Nicholson L; Long F; Castile R; Groner J
• Pilot Trial Of Phototherapy For Depression In Hospitalized Patients With Cystic Fibrosis
  Volume: 191
  01/01/2015 Authors: Kopp BT; Hayes D; Ghera P; Splaingard M
• Influence Of Hla Mismatch In The Development Of Bronchiolitis Obliterans Syndrome In Lung Transplant Recipients With Cystic Fibrosis
  Volume: 191
  01/01/2015 Authors: Kirkby S; Whitson BA; Kopp BT; Paul G; Pope-Harman A; Tobias JD; Hayes D
• Survival In Advanced Cf And Non-Cf Bronchiectasis
  Volume: 191
  01/01/2015 Authors: Hayes D; Black SM; Kirkby S; Kopp BT; Tobias JD; Mansour HM; Whitson BA
• GEOGRAPHIC VARIATIONS IN CYSTIC FIBROSIS IN THE UNITED STATES: AN ANALYSIS OF THE US CYSTIC FIBROSIS FOUNDATION PATIENT REGISTRY
  Volume: 49 Page(s): 378 - 378
  09/01/2014 Authors: Kopp BT; Nicholson L; Paul G; Tobias J; Ramanathan C; Hayes D
• AN INTRICATE LINK BEWTEEN AUTOPHAGY, MICRORNAS, AND BURKHOLDERIA CENOCEPACIA IN CYSTIC FIBROSIS
  Volume: 49 Page(s): 349 - 349
  09/01/2014 Authors: Tazi MF; Dakhlallah D; Cormet-Boyaka E; Caution K; Akhter A; Kopp BT; Piper M; Marsh C; Amer A
• INFLUENCE OF DIABETES ON SURVIVAL IN CYSTIC FIBROSIS
  Volume: 49 Page(s): 425 - 425
  09/01/2014 Authors: Hayes D; Whitson BA; Tobias JD; Kirkby S; Kopp BT; Mansour HM; Patel AV; McCoy KS
• Polysomnographic differences associated with pulmonary hypertension in patients with advanced lung disease due to cystic fibrosis.
  Lung Volume: 192 Page(s): 413 - 419
  06/01/2014 Authors: Hayes D; Daniels CJ; Kirkby S; Kopp BT; Nicholson KL; Nance AE; Splaingard ML
• Comprehensive evaluation of lung allograft function in infants after lung and heart-lung transplantation.
  J Heart Lung Transplant Volume: 33 Page(s): 507 - 513
  05/01/2014 Authors: Hayes D; Naguib A; Kirkby S; Galantowicz M; McConnell PI; Baker PB; Kopp BT; Lloyd EA; Astor TL
• Cationic antimicrobial peptides promote microbial mutagenesis and pathoadaptation in chronic infections.
  PLoS Pathog Volume: 10 Page(s): e1004083
  04/01/2014 Authors: Limoli DH; Rockel AB; Host KM; Jha A; Kopp BT; Hollis T; Wozniak DJ
• Do Cf Patients Experience Worsening Gastroesophageal Reflux As A Function Of Increasing Age?
  Volume: 189
  01/01/2014 Authors: Woodley FW; Machado RS; Hayes D; Kopp BT; Kaul A; Skaggs B; Di Lorenzo C; Mousa H
• Respiratory syncytial virus: current and emerging treatment options.
  Clinicoecon Outcomes Res Volume: 6 Page(s): 217 - 225
  01/01/2014 Authors: Turner TL; Kopp BT; Paul G; Landgrave LC; Hayes D; Thompson R
• Survival of patients with cystic fibrosis on ECMO: analysis of the Extracorporeal Life Support Organization Registry.
  Int J Clin Exp Med Volume: 7 Page(s): 1370 - 1372
  01/01/2014 Authors: Hayes D; Kopp BT; Preston TJ; Kirkby S; Tobias JD; Papadimos TJ; Whitson BA
• Cardiac fibroma, anomalous pulmonary venous course, and persistent pneumonia in a patient with Gorlin syndrome.
  Pediatr Pulmonol Volume: 49 Page(s): E7 - E9
  01/01/2014 Authors: Kopp BT; Rosen KL; O'Donovan JC; Sheikh S
• IFN- stimulates autophagy-mediated clearance of Burkholderia cenocepacia in human cystic fibrosis macrophages.
  PLoS One Volume: 9 Page(s): e96681
  01/01/2014 Authors: Assani K; Tazi MF; Amer AO; Kopp BT
• The BMPR2 missense mutation p.K230N and pulmonary arterial hypertension.
  Pediatr Pulmonol Volume: 49 Page(s): E5 - E6
  01/01/2014 Authors: Hayes D; Ramanathan C; Kopp BT
• Surveillance transbronchial biopsies in infant lung and heart-lung transplant recipients.
  Pediatr Transplant Volume: 17 Page(s): 670 - 675
  11/01/2013 Authors: Hayes D; Baker PB; Kopp BT; Kirkby S; Galantowicz M; McConnell PI; Astor TL
• Diabetic myonecrosis in a cystic fibrosis patient.
  Respir Care Volume: 58 Page(s): e123 - e125
  10/01/2013 Authors: Kopp BT; Kirkby S; Hayes D; Flanigan KM
• VITAMIN D ENHANCED AUTOPHAGIC CLEARANCE OF BURKHOLDERIA CENOCEPACIA IN CF MACROPHAGES
  Volume: 48 Page(s): 312 - 313
  10/01/2013 Authors: Kopp BT; Assani K; Amer A
• SURVIVAL OF CYSTIC FIBROSIS PATIENTS ON ECMO: ANALYSIS OF THE EXTRACORPOREAL LIFE SUPPORT ORGANIZATION REGISTRY
  Volume: 48 Page(s): 367 - 367
  10/01/2013 Authors: Hayes JD; Kopp BT; Preston TJ; Kirkby S; Mansour HM; Whitson BA
• DETRIMENTAL EFFECTS OF SECONDHAND SMOKE EXPOSURE ON INFANTS WITH CYSTIC FIBROSIS
  Volume: 48 Page(s): 373 - 374
  10/01/2013 Authors: Kopp BT; Sarzynski L; Khalfoun S; Thompson R; Hayes D; Groner J
• Light exposure and depression in hospitalized adult patients with cystic fibrosis.
  J Affect Disord Volume: 150 Page(s): 585 - 589
  09/05/2013 Authors: Kopp BT; Hayes D; Ratkiewicz M; Baron N; Splaingard M
• Right heart catheterization measuring central hemodynamics in cystic fibrosis during exercise.
  Respir Med Volume: 107 Page(s): 1365 - 1369
  09/01/2013 Authors: Hayes D; Daniels CJ; Mansour HM; Kopp BT; Yates AR; McCoy KS; Patel AV; Kirkby S
• Elevated high-sensitivity C-reactive protein in preterm infants with pulmonary colonization with Ureaplasma.
  J Thorac Dis Volume: 5 Page(s): 223 - 227
  06/01/2013 Authors: Meadows JT; Kopp BT; Shook LA; Ballard HO; Hayes D
• Autophagic Clearance Of Burkholderia Cenocepacia
  Volume: 187
  01/01/2013 Authors: Kopp BT; Assani K; Amer A
• LIGHTING UP DEPRESSION IN CYSTIC FIBROSIS
  Volume: 47 Page(s): 431 - 431
  09/01/2012 Authors: Kopp BT; Baron N; Splaingard M
• Exaggerated inflammatory responses mediated by Burkholderia cenocepacia in human macrophages derived from Cystic fibrosis patients.
  Biochem Biophys Res Commun Volume: 424 Page(s): 221 - 227
  07/27/2012 Authors: Kopp BT; Abdulrahman BA; Khweek AA; Kumar SB; Akhter A; Montione R; Tazi MF; Caution K; McCoy K; Amer AO
• Inpatient healthcare trends among adult cystic fibrosis patients in the U.S.
  Pediatr Pulmonol Volume: 47 Page(s): 245 - 251
  03/01/2012 Authors: Kopp BT; Wang W; Chisolm DJ; Kelleher KJ; McCoy KS
• Autophagy stimulation by rapamycin suppresses lung inflammation and infection by Burkholderia cenocepacia in a model of cystic fibrosis.
  Autophagy Volume: 7 Page(s): 1359 - 1370
  11/01/2011 Authors: Abdulrahman BA; Khweek AA; Akhter A; Caution K; Kotrange S; Abdelaziz DHA; Newland C; Rosales-Reyes R; Kopp B; McCoy K
• A novel exon duplication of the cystic fibrosis transmembrane conductance regulator in a patient presenting with adult-onset recurrent pancreatitis.
  Pancreas Volume: 40 Page(s): 773 - 777
  07/01/2011 Authors: Kopp BT; Pastore MT; Sturm AC; Holtzlander MJ; Westman JA
• Burkholderia cenocepacia O polysaccharide chain contributes to caspase-1-dependent IL-1beta production in macrophages.
  J Leukoc Biol Volume: 89 Page(s): 481 - 488
  03/01/2011 Authors: Kotrange S; Kopp B; Akhter A; Abdelaziz D; Abu Khweek A; Caution K; Abdulrahman B; Wewers MD; McCoy K; Marsh C
• EXAGGERATED INFLAMMATORY RESPONSES IN HUMAN CYSTIC FIBROSIS MACROPHAGES DURING BURKHOLDERIA CENOCEPACIA INFECTION
  Page(s): 260 - 260
  01/01/2011 Authors: Kopp BT; Abdulrahman B; McCoy KS; Amer AO